Meningeal hemangiopericytoma (historical)
Updates to Article Attributes
Meningeal haemangiopericytomas are rare tumours and account for less than 1% of all intracranial tumours 1. They were previously classified as angioblastic sub-type meningiomas. These tumours arise from smooth muscle perivascular pericytes of dural capillaries (pericytes of Zimmerman).
They are more aggressive than meningiomas, have a higher frequency of recurrence, and are considered a grade II tumour in the WHO Classification (c.f grade I for meningioma). Additionally, and again unlike a meningioma, they can metastasize systemically 1.
Radiographic features
Distinguishing a haemangiopericytoma from a meningioma can be difficult as they have similar appearances on both CT and MRI. Helpful features include :
- lobulated contour
- absence of calcification and hyperostosis
- invasion of the skull (common)
- multiple flow voids on MRI (need to distinguish from spoke-wheel appearance of meningioma)
- corkscrew arteries
- may have a narrow base of dural attachment
Treatment and prognosis
Total surgical excision is recommended, with adjuvant radiotherapy to reduce the incidence of recurrence.
Differential diagnosis
See also
- haemangiopericytoma - general article
-<p><strong>Meningeal haemangiopericytomas</strong> are rare tumours and account for less than 1% of all intracranial tumours <sup>1</sup>. They were previously classified as angioblastic sub-type <a href="/articles/meningioma" title="go to the article about Meningioma on Radiopaedia.org">meningiomas</a>. These tumours arise from smooth muscle perivascular pericytes of dural capillaries (pericytes of Zimmerman). </p><p>They are more aggressive than meningiomas, have a higher frequency of recurrence, and are considered a grade II tumour in the <a href="/articles/who_classification_of_cns_tumours" title="go to the article about WHO Classification of CNS tumours on Radiopaedia.org">WHO Classification</a> (c.f grade I for <a href="/articles/meningioma">meningioma</a>). Additionally, and again unlike a meningioma, they can metastasize systemically <sup>1</sup>. </p><h4>Radiographic features</h4><p>Distinguishing a haemangiopericytoma from a meningioma can be difficult as they have similar appearances on both CT and MRI. Helpful features include :</p><ul>-<li>lobulated contour</li>-<li>absence of calcification and hyperostosis</li>-<li>invasion of the skull (common) </li>-<li>multiple flow voids on MRI (need to distinguish from spoke-wheel appearance of meningioma) </li>-<li>corkscrew arteries </li>-<li>may have a narrow base of dural attachment</li>-</ul><h4>Treatment and prognosis</h4><p>Total surgical excision is recommended, with adjuvant radiotherapy to reduce the incidence of recurrence. </p><h4>Differential diagnosis</h4><ul><li><a href="/articles/meningioma" title="Meningioma">meningioma</a></li></ul><h4>See also</h4><ul><li>-<a title="Haemangiopericytoma" href="/articles/haemangiopericytoma-1">haemangiopericytoma</a> - general article</li></ul>- +<p><strong>Meningeal haemangiopericytomas</strong> are rare tumours and account for less than 1% of all intracranial tumours <sup>1</sup>. They were previously classified as angioblastic sub-type <a href="/articles/meningioma">meningiomas</a>. These tumours arise from smooth muscle perivascular pericytes of dural capillaries (pericytes of Zimmerman).</p><p>They are more aggressive than meningiomas, have a higher frequency of recurrence, and are considered a grade II tumour in the <a href="/articles/who_classification_of_cns_tumours">WHO Classification</a> (c.f grade I for <a href="/articles/meningioma">meningioma</a>). Additionally, and again unlike a meningioma, they can metastasize systemically <sup>1</sup>.</p><h4>Radiographic features</h4><p>Distinguishing a haemangiopericytoma from a meningioma can be difficult as they have similar appearances on both CT and MRI. Helpful features include :</p><ul>
- +<li>lobulated contour</li>
- +<li>absence of calcification and hyperostosis</li>
- +<li>invasion of the skull (common)</li>
- +<li>multiple flow voids on MRI (need to distinguish from spoke-wheel appearance of meningioma)</li>
- +<li>corkscrew arteries</li>
- +<li>may have a narrow base of dural attachment</li>
- +</ul><h4>Treatment and prognosis</h4><p>Total surgical excision is recommended, with adjuvant radiotherapy to reduce the incidence of recurrence.</p><h4>Differential diagnosis</h4><ul><li><a href="/articles/meningioma">meningioma</a></li></ul><h4>See also</h4><ul><li>
- +<a href="/articles/haemangiopericytoma-1">haemangiopericytoma</a> - general article</li></ul>