Mullerianosis is a rare type of choristoma, in which normal Mullerian-derived structures (endometrium, endosalpinx, and endocervix) are ectopically located in another organ (e.g. the bladder) through a developmental anomaly. Mullerianosis differs from endometriosis in that at least two types of Mullerian-derived tissue is present.
Reported cases of Mullerianosis range in presenting age from 28-53 years old. The majority have no history of pelvic surgery or caesarean section.
CT and MRI
- nonspecific multiloculated cystic mass, ranging in size from 1.0-4.5 cm
- classic location in the urinary bladder wall, although may occur elsewhere
Treatment and prognosis
Mullerianosis is generally considered benign, although there is a case report of endometrioid carcinoma arising from it 4. Symptomatic medical management has been reported to be effective.
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