The Mustard repair is a technique to correct transposition of the great arteries (TGA), and involves:
- resection of atrial septum
- creation of an atrial baffle with pericardium (or rarely synthetic material) 1
Transposition of the great arteries involves a discordance between the ventricles and their respective great arteries.
The Mustard repair is an attempt to correct this at the atrial level.
The Senning repair is functionally similar to the Mustard repair, but uses the atrial septum itself as a baffle, rather than using pericardium or synthetic material.
The arterial switch procedure is now more commonly used than either the Mustard or Senning repairs. It functionally provides an arterial rather than an atrial "switch" and anatomically corrects the abnormality. This is done partly to avoid the long-term complication of arrhythmia.
Stenosis of the baffle occurs in up to 13% of cases 2 and the extensive atrial incisions results in intra-atrial conduction delays and possible arrhythmias 3.
Congenital heart disease
There is more than one way to present the variety of congenital heart diseases. Whichever way they are categorised, it is helpful to have a working understanding of normal and fetal circulation, as well as an understanding of the segmental approach to imaging in congenital heart disease.
congenital heart disease
- normal relationship between chambers and valves
- atrioventricular valves
- outflow tract
- great vessels
- venous inflow
- anomalous valves
- abnormal relationship of chambers and valves
- atrioventricular abnormality
- great vessel connection abnormality
- conotruncal cardiac anomalies
- pentalogy of Cantrell
- Shone syndrome
- congenital heart disease - chest x-ray approach
surgical repairs (mnemonic)
- arterial switch procedure
- Blalock-Taussig shunt
- double switch procedure
- Fontan procedure
- Glenn procedure
- Mustard repair
- Norwood procedure
- Pott shunt
- pulmonary artery banding
- Rastelli procedure
- Sano shunt
- Senning repair
- total repair of tetralogy of Fallot (TOF)
- unifocalisation procedure
- Waterston shunt
- 1. Moss and Adams' heart disease in infants, children, and adolescents. Lippincott Williams & Wilkins. ISBN:0781786843. Read it at Google Books - Find it at Amazon
- 2. Diagnostic and interventional catheterization in congenital heart disease. Springer. ISBN:0792385977. Read it at Google Books - Find it at Amazon
- 3. Gatzoulis MA, Webb GD, gregory.ginsberg.uphs.upenn.edu; [P.Daubeney@rbh.nthames.nhs.uk] PEFDDP. Diagnosis and management of adult congenital heart disease. Churchill Livingstone. ISBN:0443071039. Read it at Google Books - Find it at Amazon