Neurofibromatosis type 1 (orbital manifestations)

Dr Henry Knipe et al.

Orbital manifestations of neurofibromatosis type 1 (NF1) reflects a mix of CNS, musculoskeletal and ocular disease. Usually only one orbit is affected, commonly associated with ipsilateral extracranial disease.

Pathology

NF1 manifests in the orbit in the following ways 1-5:

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Article information

rID: 40749
Section: Pathology
Synonyms or Alternate Spellings:
  • Neurofibromatosis type 1: orbital manifestations
  • NF1: orbital manifestations
  • Neurofibromatosis type 1: ophthalmic manifestations
  • Ophthalmic manifestations of NF1
  • Ophthalmic manifestations of neurofibromatosis type 1
  • Orbital manifestations of neurofibromatosis type 1

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Cases and figures

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    Case 1
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    Case 2: optic nerve gliomas
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    Case 3
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    Case 4: plexiform neurofibromas
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    Case 5: sphenoid dysplasia and neurofibromata
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