Oesophageal leiomyomatosis

Dr Henry Knipe and Radswiki et al.

Oesophageal leiomyomatosis is rare benign condition.

Epidemiology

It usually presents at childhood. There is a recognised increased female predilection.

Pathology

It is considered a hamartomatous condition and is associated with abnormal diffuse proliferation of smooth muscle fibres in distal oesophagus.

Associations

It may be associated with hereditary leiomyoma of the gastrointestinal tract in Alport syndrome.

History and etymology

This condition was first described by Hall in 1916 1.

Oesophageal pathology
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Article information

rID: 12406
Synonyms or Alternate Spellings:
  • Esophageal leiomyomatosis

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Cases and figures

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