Ossifying renal tumour of infancy

Ossifying renal tumour of infancy (ORTI) is a rare renal tumour.

  • extremely rare, <<1% of paediatric renal neoplasms (17 cases reported)
  • 6 days - 3 months
  • male predominant

Histology reveals spindle cells and osteoblastic cells in a calcified osteoid matrix. It is thought to originate from intralobar nephrogenic rests.

Abdominal radiography
Ultrasound
  • calcification is hyperechoic
  • there may be intra-tumoral flow on colour Doppler ultrasound
CT

ORTI may resemble a staghorn calculus since it originates from the renal papilla, but it enhances postcontrast.

Cases of ORTI so far have been benign, with no recurrence after resection.

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Article information

rID: 43902
Tags: kidney, rare, cases
Synonyms or Alternate Spellings:
  • Ossifying renal tumour of infants
  • Ossifying renal tumor of infancy
  • ORTI
  • Ossifying renal tumour of infancy (ORTI)
  • Ossifying renal tumor of infancy
  • Ossifying renal tumor of infants

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