Osteopathia striata, also known as Voorhoeve disease, is a rare, benign sclerosing bone dysplasia, involving the epiphysis and metaphysis of tubular bones.
Oseopathia striata can be found in any age group.
It is typically asymptomatic, although there can be associated joint discomfort.
There is an association with focal dermal hypoplasia (Goltz syndrome).
Osteopathia striata is typically bilateral, although occasionally it can be unilateral, typically in tubular bones.
Radiographically prominent vertical striations predominate in the metaphyses and epiphyses of the long bones (celery stalk metaphysis).
The differential diagnosis includes:
- 1. Roche CJ, O'keeffe DP, Lee WK et-al. Selections from the buffet of food signs in radiology. Radiographics. 22 (6): 1369-84. doi:10.1148/rg.226025521 - Pubmed citation
- 2. Levine SM, Lambiase RE, Petchprapa CN. Cortical lesions of the tibia: characteristic appearances at conventional radiography. Radiographics. 23 (1): 157-77. doi:10.1148/rg.231015088 - Pubmed citation
- 3. Gay BB, Elsas LJ, Wyly JB et-al. Osteopathia striata with cranial sclerosis. Pediatr Radiol. 1994;24 (1): 56-60. Pubmed citation
- 4. Bass HN, Weiner JR, Goldman A et-al. Osteopathia striata syndrome. Clinical, genetic and radiologic considerations. Clin Pediatr (Phila). 1980;19 (5): 369-73. Pubmed citation