Oval window atresia

Oval window atresia or congenital absence of oval window shows absent cleavage plane between the lateral semicircular canal above and cochlear promontory below associated with anomalous stapes and malpositioned facial nerve (cranial nerve VII). 

Profound conductive hearing loss in children. Normal external auditory canal.

  • oval window is covered by thin bony plate best seen on coronal plane
  • stapes is malformed (usually absent paired crura and distal incus)
  • inferomedially positioned tympanic segment of the facial nerve canal which may completely overlie expected location of oval window
  • normal external auditory canal
Share article

Article Information

rID: 47165
System: Head & Neck
Section: Pathology
Tag: cases
Synonyms or Alternate Spellings:
  • OW atresia
  • Congenital absence of oval window

Support Radiopaedia and see fewer ads

Updating… Please wait.
Loadinganimation

Alert accept

Error Unable to process the form. Check for errors and try again.

Alert accept Thank you for updating your details.