Plexogenic arteriopathy

Last revised by Dr Yuranga Weerakkody on 16 Oct 2020

Plexogenic arteriopathy has been a term used to describe a constellation of vascular changes occurring in those with pulmonary arterial hypertension. It is considered the histologic hallmark of idiopathic pulmonary arterial hypertension; it is seen in approximately 75% of cases 3. The term for the clinical situation has not been largely replaced by idiopathic pulmonary hypertension.

Radiographic features

CT

On chest CT, may been seen as small, tortuous peripheral arteries without a significant connection to pulmonary veins. Features of background pulmonary hypertension may also be present.

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Cases and figures

  • Case 1
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  • Case 2
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