Plexogenic arteriopathy

Last revised by Dr David Luong on 09 Feb 2022

Plexogenic arteriopathy has been a term used to describe a constellation of vascular changes occurring in those with pulmonary arterial hypertension. It is considered the histologic hallmark of idiopathic pulmonary arterial hypertension; it is seen in approximately 75% of cases 3. The term for the clinical situation has not been largely replaced by idiopathic pulmonary hypertension.

Radiographic features


Chest CT, may demonstrate small and tortuous peripheral arteries without a significant connection to pulmonary veins. Features of background pulmonary hypertension may also be present.

ADVERTISEMENT: Supporters see fewer/no ads

Cases and figures

  • Case 1
    Drag here to reorder.
  • Case 2
    Drag here to reorder.
  • Updating… Please wait.

     Unable to process the form. Check for errors and try again.

     Thank you for updating your details.