Plexogenic arteriopathy has been a term used to describe a constellation of vascular changes occurring in those with pulmonary arterial hypertension. It is considered the histologic hallmark of idiopathic pulmonary arterial hypertension; it is seen in approximately 75% of cases 3. The term for the clinical situation has not been largely replaced by idiopathic pulmonary hypertension.
May been seen as small, tortuous peripheral arteries without a significant connection to pulmonary veins. Features of background pulmonary hypertension may also be present.
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