Posterior semicircular canal dehiscence syndrome
Posterior semicircular canal dehiscence syndrome (PSCD) is the presence of vestibuloauditory symptoms secondary to absence of the bony covering of the posterior semicircular canal (PSC).
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Epidemiology
It is thought to be rare: in a case series of 112 patients with a high riding jugular bulb it was found in only four patients (~4%).
Clinical presentation
The main ascribed symptom is hearing impairment, with a broad spectrum of severity, from minor conductive loss to marked sensorineural deafness. The pathogenic reason for this remains unexplained.
Vertigo has been found in a number of cases of posterior semicircular canal dehiscence although a causal link remains contentious 1.
Pathology
Etiology
Dehiscence of the posterior semicircular canal has been demonstrated in the imaging context of a high-riding jugular bulb and fibrous dysplasia 1,2.
Treatment and prognosis
Optimal management remains to be determined. Prognosis is unknown.
Related pathology
Related Radiopaedia articles
Inner ear pathology
-
inner ear anatomy
-
congenital inner ear malformations
- complete labyrinthine aplasia (Michel aplasia)
- rudimentary otocyst
- cochlear aplasia
- common cavity
- incomplete partition type I (cystic cochleovestibular anomaly)
- cochlear hypoplasia
- incomplete partition type II
- incomplete partition type III (X-linked deafness)
- enlarged vestibular aqueduct
- semicircular canal dysplasia
- infection and inflammation
- neoplasms
- trauma and miscellaneous
-
congenital inner ear malformations
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