Posterior semicircular canal dehiscence syndrome (PSCD) is the presence of vestibuloauditory symptoms secondary to absence of the bony covering of the posterior semicircular canal (PSC).
On this page:
Epidemiology
It is thought to be rare: in a case series of 112 patients with a high riding jugular bulb it was found in only four patients (~4%).
Clinical presentation
The main ascribed symptom is hearing impairment, with a broad spectrum of severity, from minor conductive loss to marked sensorineural deafness. The pathogenic reason for this remains unexplained.
Vertigo has been found in a number of cases of posterior semicircular canal dehiscence although a causal link remains contentious 1.
Pathology
Etiology
Dehiscence of the posterior semicircular canal has been demonstrated in the imaging context of a high-riding jugular bulb and fibrous dysplasia 1,2.
Treatment and prognosis
Optimal management remains to be determined. Prognosis is unknown.
Unable to process the form. Check for errors and try again.