Primary cardiac tumors
Updates to Article Attributes
Body
was changed:
Primary cardiac tumours are uncommon and comprise only a small minority of all tumours that involve the heart: most are mediastinal or lung tumours that extend through the pericardium and into the heart, or metastases 1.
Epidemiology
Primary cardiac tumours have an estimated autopsy prevalence of 0.001-0.03% 2.
Pathology
Primary cardiac tumours can then be divided into:
-
benign cardiac tumours: 60-75% 1,4
- cardiac myxoma: most common in adults
- cardiac lipoma (≈10% 4, second most common in adults 6)
- cardiac rhabdomyoma: most common in children
- papillary fibroelastoma
- cardiac fibroma
- cardiac haemangioma
- cardiac paraganglioma
- pericardial teratoma (can rapidly grow despite being benign) 7,8
-
malignant cardiac tumours
-
sarcomas account for 25% of allcardiac tumours 2,6
- cardiac angiosarcoma: most common malignant primary cardiac tumour 3,9
- undifferentiated pleomorphic sarcoma of the heart
- cardiac leiomyosarcoma
- cardiac spindle cell sarcoma
- cardiac fibrosarcoma
- cardiac liposarcoma
- primary cardiac osteosarcoma: 3-9% of primary cardiac malignant tumours 9
- malignant fibrous histiocytoma of heart
- cardiac haemangiopericytoma
- primary cardiac lymphoma
- pericardial mesothelioma
-
sarcomas account for 25% of allcardiac tumours 2,6
-<a title="Cardiac sarcoma" href="/articles/cardiac-sarcoma">sarcomas</a> account for 25% of all<em> </em>cardiac tumours <sup>2,6</sup><ul>- +<a href="/articles/cardiac-sarcoma">sarcomas</a> account for 25% of all<em> </em>cardiac tumours <sup>2,6</sup><ul>
-<li><a href="/articles/undifferentied-sarcoma-of-the-heart">undifferentiated sarcoma of the heart</a></li>- +<li><a title="Cardiac undifferentiated pleomorphic sarcoma" href="/articles/cardiac-undifferentiated-pleomorphic-sarcoma">undifferentiated pleomorphic sarcoma of the heart</a></li>