Primary cardiac tumors

Changed by Yuranga Weerakkody, 20 Jul 2014

Updates to Article Attributes

Body was changed:

Primary cardiac tumours are uncommon, and comprise only a small minority of all tumour that involve the heart: most are mediastinal or lung tumours which extend through the pericardium and into the heart, or metastases 1.

Epidemiology

Primary cardiac tumours have an estimated autopsy prevalence of 0.001 - 0-0.03% 2

Pathology

Primary cardiac tumours can then be divided into:

  • -<p><strong>Primary cardiac tumours</strong> are uncommon, and comprise only a small minority of all tumour that involve the heart: most are mediastinal or lung tumours which extend through the pericardium and into the heart, or metastases <sup>1</sup>. </p><h4>Epidemiology</h4><p>Primary cardiac tumours have an estimated autopsy prevalence of 0.001 - 0.03% <sup>2</sup>. </p><h4>Pathology</h4><p>Primary cardiac tumours can then be divided into:</p><ul>
  • -<li>
  • -<a href="/articles/primary-benign-cardiac-tumours" title="Benign cardiac tumours - primary">benign cardiac tumours</a> : 60-75% <sup>1,4</sup><ul>
  • -<li>
  • -<a href="/articles/cardiac_myxoma" title="Cardiac myxoma">cardiac myxoma </a>: most common in adults</li>
  • -<li>
  • -<a href="/articles/cardiac-lipoma" title="cardiac lipoma" style="COLOR: rgb(63,117,216); TEXT-DECORATION: none">cardiac lipoma </a>(≈ 10% <sup>4</sup>, second most common in adults <sup>6</sup>)</li>
  • -<li>
  • -<a href="/articles/cardiac-rhabdomyoma" title="cardiac rhabdomyoma">cardiac rhabdomyoma</a> : most common in children</li>
  • -<li><a href="/articles/papillary-fibroelastoma" title="papillary fibroelastoma">papillary fibroelastoma</a></li>
  • -<li><a href="/articles/cardiac-fibroma" title="cardiac fibroma">cardiac fibroma</a></li>
  • -<li><a href="/articles/cardiac-haemangioma-1" title="cardiac haemangioma">cardiac haemangioma</a></li>
  • -<li>
  • -<a href="/articles/pericardial-teratoma" title="pericardial teratoma">pericardial teratoma </a>(can rapidly grow despite being benign)<a href="/articles/pericardial-teratoma" title="pericardial teratoma"> </a><sup style="PADDING-RIGHT: 0px; PADDING-LEFT: 0px; PADDING-BOTTOM: 0px; MARGIN: 0px; PADDING-TOP: 0px">7-8 </sup><ul><li><a href="/articles/fetal-pericardial-teratoma" title="Fetal pericardial teratomas">fetal pericardial teratoma</a></li></ul>
  • -</li>
  • +<p><strong>Primary cardiac tumours</strong> are uncommon, and comprise only a small minority of all tumour that involve the heart: most are mediastinal or lung tumours which extend through the pericardium and into the heart, or metastases <sup>1</sup>.</p><h4>Epidemiology</h4><p>Primary cardiac tumours have an estimated autopsy prevalence of 0.001-0.03% <sup>2</sup>. </p><h4>Pathology</h4><p>Primary cardiac tumours can then be divided into:</p><ul>
  • +<li>
  • +<a href="/articles/primary-benign-cardiac-tumours">benign cardiac tumours</a> : 60-75% <sup>1,4</sup><ul>
  • +<li>
  • +<a href="/articles/cardiac-myxoma">cardiac myxoma </a>: most common in adults</li>
  • +<li>
  • +<a href="/articles/cardiac-lipoma">cardiac lipoma </a>(≈ 10% <sup>4</sup>, second most common in adults <sup>6</sup>)</li>
  • +<li>
  • +<a href="/articles/cardiac-rhabdomyoma">cardiac rhabdomyoma</a> : most common in children</li>
  • +<li><a href="/articles/papillary-fibroelastoma-of-the-heart">papillary fibroelastoma</a></li>
  • +<li><a href="/articles/cardiac-fibroma">cardiac fibroma</a></li>
  • +<li><a href="/articles/cardiac-haemangioma-1">cardiac haemangioma</a></li>
  • +<li>
  • +<a href="/articles/pericardial-teratoma">pericardial teratoma </a>(can rapidly grow despite being benign)<a href="/articles/pericardial-teratoma"> </a><sup>7-8 </sup><ul><li><a href="/articles/fetal-pericardial-teratoma">fetal pericardial teratoma</a></li></ul>
  • +</li>
  • -</li>
  • -<li>
  • -<a href="/articles/primary-malignant-cardiac-tumours" title="Primary malignant cardiac tumours">malignant cardiac tumours</a><ul>
  • -<li>
  • +</li>
  • +<li>
  • +<a href="/articles/primary-malignant-cardiac-tumours">malignant cardiac tumours</a><ul>
  • +<li>
  • -<li>
  • -<a href="/articles/cardiac-angiosarcoma" title="Cardiac angiosarcoma">cardiac angiosarcoma</a> : most common malignant primary cardiac tumour <sup>3</sup><a href="/articles/primary-cardiac-osteosarcoma" title="primary cardiac osteosarcoma" style="COLOR: rgb(63,117,216); TEXT-DECORATION: none"></a>
  • -</li>
  • -<li><a href="/articles/primary-cardiac-osteosarcoma" title="primary cardiac osteosarcoma" style="COLOR: rgb(63,117,216); TEXT-DECORATION: none">primary cardiac osteosarcoma </a></li>
  • +<li>
  • +<a href="/articles/cardiac-angiosarcoma">cardiac angiosarcoma</a>: most common malignant primary cardiac tumour <sup>3,9</sup>
  • +</li>
  • +<li><a title="undifferentied sarcoma of the heart" href="/articles/undifferentied-sarcoma-of-the-heart">undifferentied sarcoma of the heart</a></li>
  • +<li><a title="cardiac leiomyosarcoma" href="/articles/cardiac-leiomyosarcoma">cardiac leiomyosarcoma</a></li>
  • +<li><a title="cardiac fibrosarcoma" href="/articles/cardiac-fibrosarcoma">cardiac fibrosarcoma</a></li>
  • +<li><a title="cardiac liposarcoma" href="/articles/cardiac-liposarcoma">cardiac liposarcoma</a></li>
  • +<li>
  • +<a href="/articles/primary-cardiac-osteosarcoma">primary cardiac osteosarcoma: </a>3-9% of primary cardiac malignant tumours <sup>9</sup>.</li>
  • -</li>
  • -<li>
  • -<a href="/articles/malignant-fibrous-histiocytoma-mfh-of-heart" title="malignant fibrous histiocytoma (MFH) of heart">malignant fibrous histiocytoma (MFH) of heart</a><a href="/articles/musculoskeletal-haemangiopericytoma" title="Haemangiopericytoma (MSK)" style="PADDING-RIGHT: 0px; PADDING-LEFT: 0px; PADDING-BOTTOM: 0px; MARGIN: 0px; COLOR: rgb(63,117,216); PADDING-TOP: 0px; TEXT-DECORATION: none"></a>
  • -</li>
  • -<li>
  • -<a href="/articles/cardiac-haemangiopericytoma" title="cardiac haemangiopericytoma">cardiac haemangiopericytoma</a><a href="/articles/new" title="cardiac lymphoma" style="PADDING-RIGHT: 0px; PADDING-LEFT: 0px; PADDING-BOTTOM: 0px; MARGIN: 0px; COLOR: rgb(127,127,127); PADDING-TOP: 0px; TEXT-DECORATION: none"></a>
  • -</li>
  • -<li><a href="/articles/primary-cardiac-lymphoma" title="primary cardiac lymphoma">primary cardiac lymphoma</a></li>
  • -<li><a href="/articles/pericardial-mesothelioma" title="pericardial mesothelioma">pericardial mesothelioma</a></li>
  • +</li>
  • +<li><a href="/articles/malignant-fibrous-histiocytoma-mfh-of-heart">malignant fibrous histiocytoma (MFH) of heart</a></li>
  • +<li><a href="/articles/cardiac-haemangiopericytoma">cardiac haemangiopericytoma</a></li>
  • +<li><a href="/articles/primary-cardiac-lymphoma">primary cardiac lymphoma</a></li>
  • +<li><a href="/articles/pericardial-mesothelioma">pericardial mesothelioma</a></li>
  • -</li>
  • +</li>

References changed:

  • 9. O'Donnell DH, Abbara S, Chaithiraphan V et-al. Cardiac tumors: optimal cardiac MR sequences and spectrum of imaging appearances. AJR Am J Roentgenol. 2009;193 (2): 377-87. <a href="http://dx.doi.org/10.2214/AJR.08.1895">doi:10.2214/AJR.08.1895</a> - <a href="http://www.ncbi.nlm.nih.gov/pubmed/19620434">Pubmed citation</a><span class="auto"></span>
Images Changes:

Image 1 CT (C+ arterial phase) ( update )

Caption was changed:
Case 1 -: right atrial myxoma

Image 2 Ultrasound ( update )

Caption was changed:
Case 2 -: tuberous sclerosis and cardiac rhabdomyomas

Image 3 CT (C+ arterial phase) ( update )

Caption was changed:
Case 3 -: cardiac haemangioma

ADVERTISEMENT: Supporters see fewer/no ads