Primary cardiac tumors
Updates to Article Attributes
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Primary cardiac tumours are uncommon, and comprise only a small minority of all tumour that involve the heart: most are mediastinal or lung tumours which extend through the pericardium and into the heart, or metastases 1.
Epidemiology
Primary cardiac tumours have an estimated autopsy prevalence of 0.001 - 0-0.03% 2.
Pathology
Primary cardiac tumours can then be divided into:
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benign cardiac tumours : 60-75% 1,4
- cardiac myxoma : most common in adults
- cardiac lipoma (≈ 10% 4, second most common in adults 6)
- cardiac rhabdomyoma : most common in children
- papillary fibroelastoma
- cardiac fibroma
- cardiac haemangioma
- pericardial teratoma (can rapidly grow despite being benign)7-8
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malignant cardiac tumours
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sarcomas account for 25 % of all cardiac tumours 2,6
- cardiac angiosarcoma: most common malignant primary cardiac tumour 3,9
- undifferentied sarcoma of the heart
- cardiac leiomyosarcoma
- cardiac fibrosarcoma
- cardiac liposarcoma
- primary cardiac osteosarcoma: 3-9% of primary cardiac malignant tumours 9.
- malignant fibrous histiocytoma (MFH) of heart
- cardiac haemangiopericytoma
- primary cardiac lymphoma
- pericardial mesothelioma
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sarcomas account for 25 % of all cardiac tumours 2,6
-<p><strong>Primary cardiac tumours</strong> are uncommon, and comprise only a small minority of all tumour that involve the heart: most are mediastinal or lung tumours which extend through the pericardium and into the heart, or metastases <sup>1</sup>. </p><h4>Epidemiology</h4><p>Primary cardiac tumours have an estimated autopsy prevalence of 0.001 - 0.03% <sup>2</sup>. </p><h4>Pathology</h4><p>Primary cardiac tumours can then be divided into:</p><ul>-<li>-<a href="/articles/primary-benign-cardiac-tumours" title="Benign cardiac tumours - primary">benign cardiac tumours</a> : 60-75% <sup>1,4</sup><ul>-<li>-<a href="/articles/cardiac_myxoma" title="Cardiac myxoma">cardiac myxoma </a>: most common in adults</li>-<li>-<a href="/articles/cardiac-lipoma" title="cardiac lipoma" style="COLOR: rgb(63,117,216); TEXT-DECORATION: none">cardiac lipoma </a>(≈ 10% <sup>4</sup>, second most common in adults <sup>6</sup>)</li>-<li>-<a href="/articles/cardiac-rhabdomyoma" title="cardiac rhabdomyoma">cardiac rhabdomyoma</a> : most common in children</li>-<li><a href="/articles/papillary-fibroelastoma" title="papillary fibroelastoma">papillary fibroelastoma</a></li>-<li><a href="/articles/cardiac-fibroma" title="cardiac fibroma">cardiac fibroma</a></li>-<li><a href="/articles/cardiac-haemangioma-1" title="cardiac haemangioma">cardiac haemangioma</a></li>-<li>-<a href="/articles/pericardial-teratoma" title="pericardial teratoma">pericardial teratoma </a>(can rapidly grow despite being benign)<a href="/articles/pericardial-teratoma" title="pericardial teratoma"> </a><sup style="PADDING-RIGHT: 0px; PADDING-LEFT: 0px; PADDING-BOTTOM: 0px; MARGIN: 0px; PADDING-TOP: 0px">7-8 </sup><ul><li><a href="/articles/fetal-pericardial-teratoma" title="Fetal pericardial teratomas">fetal pericardial teratoma</a></li></ul>-</li>- +<p><strong>Primary cardiac tumours</strong> are uncommon, and comprise only a small minority of all tumour that involve the heart: most are mediastinal or lung tumours which extend through the pericardium and into the heart, or metastases <sup>1</sup>.</p><h4>Epidemiology</h4><p>Primary cardiac tumours have an estimated autopsy prevalence of 0.001-0.03% <sup>2</sup>. </p><h4>Pathology</h4><p>Primary cardiac tumours can then be divided into:</p><ul>
- +<li>
- +<a href="/articles/primary-benign-cardiac-tumours">benign cardiac tumours</a> : 60-75% <sup>1,4</sup><ul>
- +<li>
- +<a href="/articles/cardiac-myxoma">cardiac myxoma </a>: most common in adults</li>
- +<li>
- +<a href="/articles/cardiac-lipoma">cardiac lipoma </a>(≈ 10% <sup>4</sup>, second most common in adults <sup>6</sup>)</li>
- +<li>
- +<a href="/articles/cardiac-rhabdomyoma">cardiac rhabdomyoma</a> : most common in children</li>
- +<li><a href="/articles/papillary-fibroelastoma-of-the-heart">papillary fibroelastoma</a></li>
- +<li><a href="/articles/cardiac-fibroma">cardiac fibroma</a></li>
- +<li><a href="/articles/cardiac-haemangioma-1">cardiac haemangioma</a></li>
- +<li>
- +<a href="/articles/pericardial-teratoma">pericardial teratoma </a>(can rapidly grow despite being benign)<a href="/articles/pericardial-teratoma"> </a><sup>7-8 </sup><ul><li><a href="/articles/fetal-pericardial-teratoma">fetal pericardial teratoma</a></li></ul>
- +</li>
-</li>-<li>-<a href="/articles/primary-malignant-cardiac-tumours" title="Primary malignant cardiac tumours">malignant cardiac tumours</a><ul>-<li>- +</li>
- +<li>
- +<a href="/articles/primary-malignant-cardiac-tumours">malignant cardiac tumours</a><ul>
- +<li>
-<li>-<a href="/articles/cardiac-angiosarcoma" title="Cardiac angiosarcoma">cardiac angiosarcoma</a> : most common malignant primary cardiac tumour <sup>3</sup><a href="/articles/primary-cardiac-osteosarcoma" title="primary cardiac osteosarcoma" style="COLOR: rgb(63,117,216); TEXT-DECORATION: none"></a>-</li>-<li><a href="/articles/primary-cardiac-osteosarcoma" title="primary cardiac osteosarcoma" style="COLOR: rgb(63,117,216); TEXT-DECORATION: none">primary cardiac osteosarcoma </a></li>- +<li>
- +<a href="/articles/cardiac-angiosarcoma">cardiac angiosarcoma</a>: most common malignant primary cardiac tumour <sup>3,9</sup>
- +</li>
- +<li><a title="undifferentied sarcoma of the heart" href="/articles/undifferentied-sarcoma-of-the-heart">undifferentied sarcoma of the heart</a></li>
- +<li><a title="cardiac leiomyosarcoma" href="/articles/cardiac-leiomyosarcoma">cardiac leiomyosarcoma</a></li>
- +<li><a title="cardiac fibrosarcoma" href="/articles/cardiac-fibrosarcoma">cardiac fibrosarcoma</a></li>
- +<li><a title="cardiac liposarcoma" href="/articles/cardiac-liposarcoma">cardiac liposarcoma</a></li>
- +<li>
- +<a href="/articles/primary-cardiac-osteosarcoma">primary cardiac osteosarcoma: </a>3-9% of primary cardiac malignant tumours <sup>9</sup>.</li>
-</li>-<li>-<a href="/articles/malignant-fibrous-histiocytoma-mfh-of-heart" title="malignant fibrous histiocytoma (MFH) of heart">malignant fibrous histiocytoma (MFH) of heart</a><a href="/articles/musculoskeletal-haemangiopericytoma" title="Haemangiopericytoma (MSK)" style="PADDING-RIGHT: 0px; PADDING-LEFT: 0px; PADDING-BOTTOM: 0px; MARGIN: 0px; COLOR: rgb(63,117,216); PADDING-TOP: 0px; TEXT-DECORATION: none"></a>-</li>-<li>-<a href="/articles/cardiac-haemangiopericytoma" title="cardiac haemangiopericytoma">cardiac haemangiopericytoma</a><a href="/articles/new" title="cardiac lymphoma" style="PADDING-RIGHT: 0px; PADDING-LEFT: 0px; PADDING-BOTTOM: 0px; MARGIN: 0px; COLOR: rgb(127,127,127); PADDING-TOP: 0px; TEXT-DECORATION: none"></a>-</li>-<li><a href="/articles/primary-cardiac-lymphoma" title="primary cardiac lymphoma">primary cardiac lymphoma</a></li>-<li><a href="/articles/pericardial-mesothelioma" title="pericardial mesothelioma">pericardial mesothelioma</a></li>- +</li>
- +<li><a href="/articles/malignant-fibrous-histiocytoma-mfh-of-heart">malignant fibrous histiocytoma (MFH) of heart</a></li>
- +<li><a href="/articles/cardiac-haemangiopericytoma">cardiac haemangiopericytoma</a></li>
- +<li><a href="/articles/primary-cardiac-lymphoma">primary cardiac lymphoma</a></li>
- +<li><a href="/articles/pericardial-mesothelioma">pericardial mesothelioma</a></li>
-</li>- +</li>
References changed:
- 9. O'Donnell DH, Abbara S, Chaithiraphan V et-al. Cardiac tumors: optimal cardiac MR sequences and spectrum of imaging appearances. AJR Am J Roentgenol. 2009;193 (2): 377-87. <a href="http://dx.doi.org/10.2214/AJR.08.1895">doi:10.2214/AJR.08.1895</a> - <a href="http://www.ncbi.nlm.nih.gov/pubmed/19620434">Pubmed citation</a><span class="auto"></span>
Images Changes:
Image 1 CT (C+ arterial phase) ( update )
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Case 1 -: right atrial myxoma
Image 2 Ultrasound ( update )
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Case 2 -: tuberous sclerosis and cardiac rhabdomyomas
Image 3 CT (C+ arterial phase) ( update )
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Case 3 -: cardiac haemangioma