Primary pleural lymphoma

Last revised by Mohammad Taghi Niknejad on 5 Jul 2022

Primary pleural lymphoma is extremely rare, especially in immunocompetent patients.

Primary pleural lymphoma accounts for <0.5% of all non-Hodgkin lymphoma 2 and ~2.5% of primary chest wall tumors 4

Primary pleural lymphoma may be Hodgkin or non-Hodgkin lymphoma with diffuse large B-cell accounting for the majority (60%) of cases 4

Primary pleural lymphoma has been described in the setting of chronic inflammation or in immunocompromised patients 1:

Case reports exist of primary pleural lymphoma in immunocompetent patients with other proposed causative factors 4:

Primary pleural lymphoma may presents with non-specific features 3,4:

Other types of pleural tumors should be considered. 

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