Citation, DOI, disclosures and article data
Citation:
Weerakkody Y, Hapugoda S, Primary pulmonary angiosarcoma. Reference article, Radiopaedia.org (Accessed on 11 Dec 2024) https://doi.org/10.53347/rID-29931
Primary pulmonary angiosarcoma is an extremely rare tumor that can involve the lung. It is considered the rarer form of angiosarcoma involving the lung.
Like other angiosarcomas, they are derived from vascular endothelial cells.
Treatment and prognosis
Varying managements options have been described ranging from surgery to chemotherapeutic regimens to radiotherapy to immunotherapy of a combination.
But despite this the prognosis is considered to be dismal.
Consider:
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1. Kojima K, Okamoto I, Ushijima S et-al. Successful treatment of primary pulmonary angiosarcoma. Chest. 2004;124 (6): 2397-400. Pubmed citation
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2. Duck L, Baurain JF, Machiels JP. Treatment of a primary pulmonary angiosarcoma. Chest. 2004;126 (1): 317-8. doi:10.1378/chest.126.1.317 - Pubmed citation
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3. Obeso Carillo GA, García Fontán EM, Cañizares Carretero MÁ et-al. Primary pulmonary angiosarcoma, an exceptional neoplasm with a poor prognosis: reports of two cases and review of the literature. Gen Thorac Cardiovasc Surg. 2013;61 (11): 643-7. doi:10.1007/s11748-012-0200-6 - Pubmed citation
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4. Chen YB, Guo LC, Yang L et-al. Angiosarcoma of the lung: 2 cases report and literature reviewed. Lung Cancer. 2010;70 (3): 352-6. doi:10.1016/j.lungcan.2010.09.002 - Pubmed citation
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5. Patel AM, Ryu JH. Angiosarcoma in the lung. Chest. 1993;103 (5): 1531-5. Pubmed citation
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