Pulmonary sequestration (extralobar)

Extralobar pulmonary sequestration (ELS) is a subtype of pulmonary sequestration, the other type being intralobar pulmonary sequestration (ILS).

It is usually encountered in infants, most being diagnosed before six months. It is more common in male (M:F 4:1).

Extralobar pulmonary sequestration is the less common type of pulmonary sequestration, accounting only for 15-25%.

ELS is covered by its own pleura and this is what differentiates ELS from ILS. 

ELS receives vascular supply mainly from the aorta (thoracic or abdominal) or from other arterial vessels (splenic, subclavian, gastric, intercostal or multiple vessels) and venous drainage can be either systemic or pulmonary. 

Location

There is strong predilection towards the left lower lobe (65-90%).

Associations
CT
  • well marginated mass
  • usually homogeneous, often without internal gas
  • may contain cystic areas
  • systemic arterial supply 4

Surgical excision is the mainstay of treatment.

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Article Information

rID: 26985
Systems: Paediatrics, Chest
Tag: cases
Synonyms or Alternate Spellings:
  • Extralobar sequestration
  • Extralobar pulmonary sequestration

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