Pyloric atresia is a rare congenital malformation of the stomach with complete obstruction of the pyloric lumen. This may be due to one or multiple webs, a solid soft tissue cord with no lumen replacing the pyloric canal, or no connection between the stomach and proximal duodenum 2. In pyloric stenosis there is an incomplete obstruction of the pyloric lumen.
On this page:
Clinical presentation
Patients present in early life with nonbilious vomiting and are unable to tolerate feeding.
Radiographic features
Plain radiograph
Abdominal radiographs classically show a gas filled distended stomach with absence of distal bowel gas, giving rise to single bubble sign.
Ultrasound
Prenatally, a 'single bubble' may be seen with a fluid filled stomach but none distally. Antenatally, the absence of pyloric muscle normal echotexture, absence of the pyloric canal, failure of the pylorus to open, and a thin long pylorus, may additionally be appreciated, 1,3.
Treatment and prognosis
Surgical correction is needed which may involve excision or canalization. However, prognosis is determined by other associated abnormalities. Patients may have intestinal and colonic atresia as well.
Unable to process the form. Check for errors and try again.