Retroperitoneal malignant fibrous histiocytoma

retroperitoneal malignant fibrous histiocytoma is an uncommon tumour overall but is considered as one of the most common types of primary retroperitoneal neoplasms. Only 15% of all malignant fibrous histiocytomas occur within the retroperitoneum

They are categorised as sarcomas and are often high grade tumours. They occur with predominance in men.

Pathology

There are six histological subtypes: storiform, pleomorphic, myxoid, giant cell, inflammatory and angiomatoid. Most metastasize and common sites include lung and lymph nodes.

Radiographic features

Imaging is not characteristic and clarification pathologically is required. Reassessment of malignant fibrous histiocytoma diagnosis in some series result in re-classification as dedifferentiated liposarcomas.

25% of cases include dystrophic calcification which is uncommon amongst the remaining primary retroperitoneal malignancies.

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Article Information

rID: 6338
Synonyms or Alternate Spellings:

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