Articles
Articles are a collaborative effort to provide a single canonical page on all topics relevant to the practice of radiology. As such, articles are written and edited by countless contributing members over a period of time. A global group of dedicated editors oversee accuracy, consulting with expert advisers, and constantly reviewing additions.
758 results found
Article
Rhabdomyosarcoma (cardiac)
Cardiac rhabdomyosarcoma is a muscular tumor that arises in the heart.
Epidemiology
They account for only 4-7% of cardiac sarcomas overall but are the most common cardiac malignancy in infants and children. There is a slight male predilection.
Pathology
Location
Cardiac rhabdomyosarcoma has...
Article
Cardiac conduction devices
Implantable cardiac conduction devices (also known as cardiac implantable electronic devices or CIEDs) are a very common medical device of the thorax, with over one million implanted in the United States of America alone.
There are two major types of cardiac conduction devices: pacemakers and a...
Article
Cardiac lipoma
Cardiac lipomas are uncommon benign primary cardiac neoplasms although they are considered the commonest non-myxomatous benign primary cardiac tumor 8.
Epidemiology
They have no defined age or sex distribution.
Clinical presentation
They are soft and may grow to a large size without causing ...
Article
Cardiac herniation
Cardiac herniation refers to herniation of the heart outside its expected position. It can be intrathoracic or extrathoracic.
Pathology
A cardiac herniation secondary to pericardial rupture is rare, but a highly lethal injury with most patients dying before arrival at a hospital.
Diagnosis in...
Article
Cardiac fibroma
Cardiac fibromas, also known as cardiac fibromatosis, are benign congenital cardiac tumors that usually manifest in children.
Epidemiology
Cardiac fibromas are tumors that primarily affect children (most cases are detected in infants or in utero) with a ratio of 4:1 compared with adults 5. Th...
Article
Cardiac angiosarcoma
Cardiac angiosarcomas are the most common sarcoma involving the heart (see cardiac tumors).
Please refer to the article on angiosarcomas for a general discussion about this entity.
Epidemiology
They occur slightly more frequently in males.
Clinical presentation
Patients usually present wi...
Article
Arrhythmogenic right ventricular cardiomyopathy diagnostic criteria
For the diagnosis of arrhythmogenic right ventricular cardiomyopathy (ARVC) to be made, patients must have either two major criteria, one major and two minor criteria, or four minor criteria.
Major criteria
global or regional dysfunction and structural alterations:
severe dilatation of the ri...
Article
Behçet disease
Behçet disease is a multisystemic and chronic inflammatory vasculitis of unknown etiology.
Epidemiology
The mean age at which Behçet disease occurs is 20-30 years. The disease is most prevalent in the Mediterranean region, Middle East and East Asia. The highest incidence has been reported in T...
Article
HIV/AIDS (cardiovascular manifestations)
Cardiovascular manifestations are seen with increased frequency in the HIV/AIDS adult population, and include:
pericardial effusions
dilated cardiomyopathy (prevalence 8-30%)
endocarditis: either infective or non-bacterial thrombotic (marantic) which is associated with malignancy or HIV wasti...
Article
Left ventricular pseudoaneurysm
Left ventricular pseudoaneurysms are false aneurysms that result from contained myocardial rupture, and are a rare complication of myocardial infarction (MI). They should not be confused with left ventricular aneurysms, which are true aneurysms containing all the layers (endocardium, myocardium,...
Article
Echogenic intracardiac focus
Echogenic intracardiac focus (EIF) is a relatively common sonographic observation that may be present on an antenatal ultrasound scan.
Epidemiology
They are thought to be present in ~4-5% of karyotypically normal fetuses. They may be more common in the Asian population 5.
Associations
trisom...
Article
Technetium-99m agents
Technetium agents based on the technetium-99m (Tc-99m) radioisotope are frequently used agents in medical imaging. A radiopharmaceutical labeled with Tc-99m constitutes a co-ordination complex in which ligands bond to a central atom of Tc-99m by co-ordinate covalent bonds 4 .
The radioactive te...
Article
Duke criteria for infective endocarditis
The Duke criteria are a set of clinical criteria set forward for the diagnosis of infective endocarditis
For diagnosis the requirement is:
2 major and 1 minor criterion or
1 major and 3 minor criteria or
5 minor criteria
For adequate diagnostic sensitivity, transesophageal echocardiography...
Article
Cor triatriatum
Cor triatriatum is an extremely rare and serious congenital cardiac anomaly.
Epidemiology
It is thought to account for ~0.1% of all congenital cardiac anomalies 3,4.
Clinical presentation
Clinical presentation depends on:
degree of stenosis in the fibromuscular membrane
the integrity of ...
Article
Papillary fibroelastoma of the heart
Papillary fibroelastomas are rare benign primary cardiac tumors. However, of the primary cardiac tumors, they are one of the commonest to occur in relation to the cardiac valves (may account for 75% of valvular tumors 10).
Epidemiology
Its estimated prevalence ranges between <0.01 to 0.33% 5....
Article
Pediatric cardiovascular procedures
A number of pediatric cardiovascular procedures are encountered when reporting pediatric imaging. They include:
Blalock-Taussig (BT) shunt
classic: end to side subclavian to ipsilateral pulmonary arterial anastomosis
modified: graft anastomosis
Waterston shunt
Sano shunt: right ventricle to...
Article
Fetal echocardiography views
A standard fetal echocardiogram consists of several specific views which can be obtained to optimize visualization of different structures and anomalies. They include:
Basic views
abdominal situs view / transverse view of abdomen
four chamber view
left ventricular outflow tract ...
Article
Endocardial fibroelastosis
Endocardial fibroelastosis (EFE) is a rare cardiac condition which is classically described in the pediatric population (typically first two years). It is one of the causes in infants of unexplained heart failure.
Epidemiology
Associations
mitral valve abnormalities: e.g mitral regurgitation
...
Article
Carcinoid heart disease
Carcinoid heart disease, also known as Hedinger syndrome, is a known complication of carcinoid tumors, and is particularly prevalent in patients who develop carcinoid syndrome.
Epidemiology
Cardiac lesions are present in approximately 50% of patients with carcinoid syndrome 1.
Clinical presen...
Article
Mitral valve calcification
Mitral valve calcification can refer to 1
mitral annular calcification (MAC)
mitral valve leaflet calcification (MVL)
caseous calcification of the mitral annulus
Article
Sinus of Valsalva aneurysm
A sinus of Valsalva aneurysm refers to abnormal dilatation of the sinus of valsalva and is a cause of thoracic aortic dilatation. Sinus of Valsalva aneurysms arise from one of the aortic sinuses. They are either congenital or acquired.
Epidemiology
There is a male predilection (M:F ratio being...
Article
Differential diagnosis for a small cardiothoracic ratio
A small cardiothoracic ratio (CTR) is defined as <42%/0.42 when assessed on a PA chest radiograph, and is often called small heart syndrome. A pathologically-small heart is also known as microcardia.
It can be due to/associated with a number of entities:
adrenal insufficiency, e.g. Addison...
Article
Extracorporeal membrane oxygenation
Extracorporeal membrane oxygenation (ECMO) is used as a modified pulmonary or cardiopulmonary bypass technique in those with severe cardiac and/or respiratory failure refractory to conventional ventilatory support and medical intervention 1,3. There are two access paths for extracorporeal life s...
Article
Delayed myocardial enhancement on MRI (differential)
Delayed myocardial enhancement can occur in cardiac MR assessment due to a number of causes.
They include:
myocardial ischemia: typically subendocardial and follows a vascular territory 1
non-ischemic cardiomyopathies
hypertrophic cardiomyopathy
non-ischemic dilated cardiomyopathy
arrhythm...
Article
Anomalous left coronary artery from the pulmonary artery
Anomalous left coronary artery from the pulmonary artery (ALCAPA), also known as Bland-White-Garland syndrome (BWG), is a rare congenital coronary artery anomaly and is considered one of the most severe of such anomalies.
There are two forms, based on the onset of the disease, each of which has...
Article
Eosinophilic granulomatosis with polyangiitis
Eosinophilic granulomatosis with polyangiitis (EGPA), previously known as Churg-Strauss syndrome, is a small-vessel necrotizing vasculitis usually involving the respiratory tract, and thus also classified under the spectrum of eosinophilic lung disease and as a type of pulmonary angiitis and gr...
Article
Sarcoidosis (cardiac manifestations)
Cardiac involvement of sarcoidosis is a manifestation of sarcoidosis which is often asymptomatic, although can be associated with high mortality 8. Autopsy studies show prevalence of ~25% cardiac involvement, yet only 5-10% are found symptomatic 1,2.
Sarcoidosis is a multisystem disorder chara...
Article
Lutembacher syndrome
Lutembacher syndrome refers to the association of an atrial septal defect (ASD) with mitral stenosis. Both the defects can be either congenital or acquired.
History and etymology
It is named after Rene Lutembacher 4.
Article
Eisenmenger complex
Eisenmenger complex is a specific subset of Eisenmenger syndrome, and consists of:
ventricular septal defect (VSD)
severe pulmonary arterial hypertension resulting in
shunt reversal and cyanosis
Article
Enlarged azygos vein
An enlarged/dilated azygos vein may result from a number of physiological as well as pathological causes. The enlarged azygos vein may be seen as a widened right paratracheal/paraspinal stripe on a frontal chest radiograph.
Terminology
Spelling it "azygous" when referring to the vein is incorr...
Article
Williams syndrome
Williams syndrome (WS), sometimes called Williams-Beuren syndrome, is characterized by some or all of the following features:
craniofacial dysmorphism (e.g. elfin facies)
oral abnormalities
short stature (50% of cases)
mild to moderate intellectual disability
supravalvular aortic stenosis ...
Article
Marfan syndrome
Marfan syndrome is a multisystem connective tissue disease caused by a defect in the protein fibrillin 1, encoded by the FBN1 gene. Cardiovascular involvement with aortic root dilatation and dissection is the most feared complication of the disease.
Epidemiology
The estimated prevalence is aro...
Article
Primary malignant cardiac tumors
Primary malignant cardiac tumors are rare and account for only ~25% of primary cardiac tumors, and only a small proportion of all malignant tumors which involve the heart: direct extension of adjacent tumors or metastatic deposits are far more common.
Pathology
Histological types include 1:
...
Article
Primary benign cardiac tumors
Primary benign cardiac tumors are much less common than secondary metastatic deposits. However, they are more likely when a cardiac mass is seen outside of the setting of terminal metastatic disease. Tumors include 1,2:
cardiac myxoma
most common in adults
accounts for ~50% of all primary ben...
Article
Primary cardiac tumors
Primary cardiac tumors are uncommon and comprise only a small minority of all tumors that involve the heart: most are mediastinal or lung tumors that extend through the pericardium and into the heart, or metastases 1.
Epidemiology
Primary cardiac tumors have an estimated autopsy prevalence of ...
Article
Kommerell diverticulum
Kommerell diverticula occur in some anomalies of the aortic arch system. It usually refers to the bulbous configuration of the origin of an aberrant left subclavian artery in the setting of a right-sided aortic arch. However, it was originally described as a diverticular outpouching at the origi...
Article
Coronary arteries
The coronary arteries arise from the aortic sinuses immediately distal (superior) to the aortic valve and supply the myocardium of the heart with oxygenated blood. The arteries branch to encircle the heart covering its surface with a lacy network, perhaps resembling a slightly crooked crown.
Gr...
Article
Right coronary artery
The right coronary artery (RCA) is one of the two main coronary arteries that supply the heart with oxygenated blood.
Gross anatomy
Origin
The right coronary artery arises from its ostium in the right sinus of Valsalva, found between the aortic valve annulus and the sinotubular junction.
C...
Article
Enlarged pulmonary trunk on chest radiography (differential)
The differential of an enlarged pulmonary trunk/main pulmonary artery on chest radiography includes:
normal
may appear prominent in young patients especially women
projectional
rotation
lordotic view
rotation of the heart
pectus excavatum
left lower lobe collapse
pulmonary arterial hyp...
Article
Pulmonary hypertension (2003 classification)
There are numerous causes of pulmonary hypertension, and thus not surprisingly there have been many classification systems.
In 2003, the 3rd World Symposium on PAH met in Venice and produced an updated classification system (this has been further revised in the Dana Point classification of pulm...
Article
Idiopathic pulmonary arterial hypertension
Idiopathic pulmonary arterial hypertension is uncommon, representing only a tiny fraction of all cases of pulmonary arterial hypertension, which has a very long list of secondary causes (see causes of pulmonary arterial hypertension).
Terminology
Older terms for this entity include primary pul...
Article
Pulmonary hypertension (differential)
Pulmonary hypertension has many causes, and these can be divided in many ways. A simple and systematic approach is to proceed along the cardiopulmonary pulmonary circulation, as causes are found at each site (for a more official classification system see 2003 third world symposium on pulmonary a...
Article
Blalock-Taussig shunt
Blalock-Taussig shunt, also known as Blalock-Thomas-Taussig shunt, is a palliative procedure designed to increase pulmonary arterial blood flow in patients with right ventricular outflow tract obstruction (e.g. tetralogy of Fallot) or during initial staged repair of hypoplastic left heart syndro...
Article
Waterston shunt
A Waterston shunt is a form of palliative surgery performed in patients with tetralogy of Fallot prior to the ability to repair the defect. It consists of a shunt formed between the ascending aorta and the right pulmonary artery.
This does not relieve the right ventricular outflow obstruction, ...
Article
Potts shunt
A Potts shunt is a form of palliative surgery performed in patients with tetralogy of Fallot prior to the ability to repair the defect. It consists of a shunt formed between the descending thoracic aorta and the left pulmonary artery.
This does not relieve the right ventricular outflow obstruct...
Article
Pink tetralogy of Fallot
Pink tetralogy of Fallot refers to a tetralogy of Fallot in which the degree of right ventricular outflow obstruction is minimal, resulting no significant right to left shunt, and therefore no cyanosis. Symptoms are mild and presentation may be delayed, even into adulthood.
See also
tetralogy ...
Article
Pentalogy of Fallot
The pentalogy of Fallot is a variant of the more common tetralogy of Fallot, comprising the classic four features with the addition of an atrial septal defect or patent ductus arteriosus:
ventricular septal defect (VSD)
right ventricular outlfow tract narrowing or complete obstruction
right ...
Article
Cyanotic congenital heart disease
A number of entities can present as cyanotic congenital heart disease. These can be divided into those with increased (pulmonary plethora) or decreased pulmonary vascularity:
increased pulmonary vascularity
total anomalous pulmonary venous return (TAPVR) (types I and II)
transposition of the ...
Article
Acyanotic congenital heart disease
Acyanotic congenital heart disease comprises numerous etiologies, which can be divided into those with increased pulmonary vascularity (pulmonary plethora) and those with normal vascularity:
increased pulmonary vascularity
ventricular septal defect (VSD)
atrial septal defect (ASD)
atrioventr...
Article
Normal contours of the cardiomediastinum on chest radiography
A detailed understanding of the structures that make up the normal contours of the heart and mediastinum (cardiomediastinal contour) on chest radiography is essential if abnormalities are to be detected.
Frontal view (PA/AP)
Right cardiomediastinal contour
From superior to inferior:
right p...
Article
Congenital heart disease chest x-ray (an approach)
With the advent of echocardiography, and cardiac CT and MRI, the role of chest x-rays in evaluating congenital heart disease has been largely relegated to one of historical and academic interest. However, they continue to crop up in radiology exams. In most instances a definite diagnosis cannot ...
Article
Double density sign (osteoid osteoma)
The double density sign, also sometimes clumsily referred to as the hotter spot within hot area sign, is a bone scan sign of an osteoid osteoma.
It refers to a central focus of intense uptake (the nidus) within a surrounding lower, but nonetheless increased uptake, rim.
See also
double densit...
Article
Pulmonary artery atresia
Pulmonary artery atresia (or sometimes known as pulmonary atresia) is a congenital cardiovascular anomaly in which there is complete disruption between the right ventricular outflow tract (RVOT) and the pulmonary trunk.
Epidemiology
The estimated incidence is 1 in 10,000 births.
Pathology
Th...
Article
Pericarditis
Pericarditis is defined as inflammation of the pericardium. It is normally found in association with cardiac, thoracic or wider systemic pathology and it is unusual to manifest on its own.
Epidemiology
Associations
camptodactyly arthropathy coxa vara pericarditis syndrome
Diagnosis
The diag...
Article
Restrictive cardiomyopathy
Restrictive cardiomyopathy is the least common subtype of cardiomyopathy and is characterized by a marked decrease in ventricular compliance.
Clinical presentation
Patients can present with symptoms and signs of left ventricular failure and/or right ventricular failure 9.
Pathology
It is p...
Article
Intraventricular
Intraventricular is a term used to denote lesions/processes that occur within either the ventricles of the brain or the ventricles of the heart.
In both cases, most lesions actually arise from the surrounding brain parenchyma/heart muscle and grow exophytically into the ventricles.
See also
...
Article
Pericardial effusion
Pericardial effusions occur when excess fluid collects in the pericardial space (a normal pericardial sac contains approximately 30-50 mL of fluid).
Epidemiology
There is no single demographic affected, as there are many underlying causes of pericardial effusion.
Clinical presentation
Clinic...
Article
Rheumatic heart disease
Rheumatic heart disease (not to be confused with rheumatoid heart disease) may refer to either the acute cardiac involvement or chronic cardiac sequelae following rheumatic fever. Carditis is a major Revised Jones criterion of rheumatic fever.
Epidemiology
Risk factors include:
socioeconomic ...
Article
Cardiac rhabdomyoma
Cardiac rhabdomyomas are a type of benign myocardial tumor and are considered the most common fetal cardiac tumor. They have a strong association with tuberous sclerosis.
Epidemiology
Cardiac rhabdomyomas are often multiple and can represent up to 90% of cardiac tumors in the pediatric populat...
Article
Mustard repair
The Mustard repair is a technique to correct transposition of the great arteries (TGA), and involves:
resection of atrial septum
creation of an atrial baffle with a prosthetic material usually. 1,2
Rationale
Transposition of the great arteries involves a discordance between the ventricles a...
Article
Arrhythmogenic right ventricular cardiomyopathy
Arrhythmogenic right ventricular cardiomyopathy (ARVC), also referred to as arrhythmogenic right ventricular dysplasia (ARVD) or simply arrhythmogenic cardiomyopathy, is a cardiomyopathy that is one of the more common causes of sudden cardiac death in young patients.
Epidemiology
The estimate...
Article
Congenital pulmonary stenosis
Congenital pulmonary stenosis refers to congenital narrowing of the right ventricular outflow tract, pulmonary valve, or pulmonary artery.
See pulmonary valve stenosis for a general discussion about this valvulopathy.
Epidemiology
The estimated incidence is 1 in 2000 births.
Associations
Co...
Article
Congenital aortic stenosis
Congenital aortic stenosis broadly refers to a congenital narrowing of the aortic lumen. Although the term can mean narrowing at any point, it often relates to a narrowing of the aortic valve. As a broad group, there can be some overlap with ascending aortic coarctation depending on the definiti...
Article
Kawasaki disease
Kawasaki disease is a small to medium vessel vasculitis predominantly affecting young children. It can affect any organ but there is a predilection for the coronary vessels.
Epidemiology
Japan has the highest incidence in the world, with an annual incidence of 3 per 1000 children under the age...
Article
Double outlet right ventricle
Double outlet right ventricle (DORV) is a congenital cardiac anomaly where both the aorta and pulmonary trunk arise from the morphologically right ventricle. It is reported to account for ~2% of congenital cardiac defects 1. It is usually classed as a conotruncal anomaly. There is almost always ...
Article
Cardiomyopathy (WHO/ISFC 1995 classification)
Cardiomyopathy classification separates the various cardiomyopathies into several subtypes. Cardiomyopathy is defined as a "disease of the myocardium with associated cardiac dysfunction".
It was initially classified according to the 1995 World Health Organizatiοn / International Society and Fed...
Article
Hypoplastic left heart syndrome
Hypoplastic left heart syndrome (HLHS) is a cyanotic congenital cardiac anomaly where affected individuals can have profound cyanosis and cardiac failure.
It is one of the commonest causes for a neonate to present with congestive cardiac failure and the 4th most frequent cardiac anomaly to mani...
Article
Polyarteritis nodosa
Polyarteritis nodosa is a systemic inflammatory necrotizing vasculitis that involves small to medium-sized arteries (larger than arterioles).
Epidemiology
Polyarteritis nodosa is more common in males and typically presents around the 5th to 7th decades. 20-30% of patients are hepatitis B anti...
Article
Total anomalous pulmonary venous return
Total anomalous pulmonary venous return (TAPVR) is a cyanotic congenital heart anomaly with abnormal drainage anatomy of the entire pulmonary venous system. This contrasts with partial anomalous pulmonary venous return (PAPVR) where only part of the pulmonary venous anatomy is abnormal.
In TAPV...
Article
Truncus arteriosus
Truncus arteriosus is a cyanotic congenital heart anomaly in which a single trunk supplies both the pulmonary and systemic circulation, instead of a separate aorta and a pulmonary trunk. It is usually classified as a conotruncal anomaly.
It accounts for up to 2% of congenital cardiac anomalies ...
Article
Tricuspid atresia
Tricuspid atresia is a cyanotic congenital cardiac anomaly which is characterized by agenesis of the tricuspid valve and right ventricular inlet. There is almost always an obligatory intra-atrial connection through either an ASD or patent foramen ovale (PFO) in order for circulation to be comple...
Article
Transposition of the great arteries
Transposition of the great arteries (TGA), also known as transposition of the great vessels (TGV), is the most common cyanotic congenital cardiac anomaly presenting during the newborn period, with cyanosis in the first 24 hours of life.
It occurs as a result of ventriculoarterial discordance, w...
Article
Heart
The heart is a hollow, muscular organ of the middle mediastinum, designed to pump oxygenated blood around the systemic circulation and deoxygenated blood around the pulmonary circulation.
Gross anatomy
The heart has a somewhat pyramidal form and is enclosed by the pericardium. Its base (roughl...
Article
Ebstein anomaly
Ebstein anomaly is an uncommon congenital cardiac anomaly, characterized by a variable developmental anomaly of the tricuspid valve.
Epidemiology
The anomaly accounts for only ~0.5% of congenital cardiac defects 6,7, although it is the most common cause of congenital tricuspid regurgitation. T...
Article
Tetralogy of Fallot
Tetralogy of Fallot (TOF) is the most common cyanotic congenital heart condition with many cases presenting after the newborn period. It has been classically characterized by the combination of ventricular septal defect (VSD), right ventricular outflow tract obstruction (RVOTO), overriding aorta...
Article
Patent ductus arteriosus
Patent ductus arteriosus or arteriosum (PDA) is a congenital cardiac anomaly where there is persistent patency of the ductus arteriosus, a normal connection of the fetal circulation between the aorta and the pulmonary arterial system that develops from the 6th aortic arch.
Epidemiology
Patent ...
Article
Atrioventricular septal defect
Atrioventricular septal defects (AVSDs), also known as atrioventricular canal defects or endocardial cushion defects, comprise a relatively wide range of defects involving the atrial septum, ventricular septum, and one or both of the tricuspid or mitral valve. They can represent 2-7% of congenit...
Article
Holt-Oram syndrome
Holt-Oram syndrome (HOS) is an autosomal dominant syndrome that results in congenital heart defects and upper limb anomalies:
congenital heart defects
atrial septal defect (ASD) (commonest cardiac defect 4)
ventricular septal defect (VSD)
aortic coarctation
upper limb...
Article
Ventricular septal defect
Ventricular septal defects (VSD) represent a hole or pathway in the interventricular septum that allows for communication between the right and left ventricles. It typically results in a left-to-right shunt.
Epidemiology
They represent one of the most common congenital cardiac anomalies and ma...
Article
Causes of pulseless electrical activity (mnemonic)
Pulseless electrical activity is a very disconcerting emergency medical scenario with very high mortality unless its etiology can be quickly ascertained and corrected. A mnemonic to remember the different causes of pulseless electrical activity is:
MAD (triple H) CAT
Mnemonic
M: massive pulmo...
Article
Hypertrophic cardiomyopathy
Hypertrophic cardiomyopathy (HCM) is a type of cardiomyopathy defined by left ventricular hypertrophy which cannot otherwise be explained by another cardiac or systemic disease. It is the leading cause of sudden cardiac death in infants, teenagers, and young adults.
Terminology
Although hypert...
Article
Dilated cardiomyopathy
Dilated cardiomyopathy (DCM) is defined as left ventricular chamber dilation with decreased systolic function (FEVG <40%) in the absence of coronary artery disease or conditions that impose a chronic pressure overload. There may also be right ventricular dysfunction. Causes are related to intrin...
Article
Tuberous sclerosis (diagnostic criteria)
The tuberous sclerosis diagnostic criteria have been developed to aid the diagnosis of tuberous sclerosis and have been updated in 2012 by the International Tuberous Sclerosis Complex Consensus Group (at time of writing - 2019) 1.
Criteria
Genetic criteria
The identification of either a TSC1...
Article
Atrial septal defect
Atrial septal defect (ASD) is the second most common congenital heart defect after ventricular septal defects (VSDs) and the most common to become symptomatic in adulthood.
They are characterized by an abnormal opening in the atrial septum allowing communication between the right and left atria...
Article
Saddle pulmonary embolism
Saddle pulmonary embolism commonly refers to a large pulmonary embolism that straddles the bifurcation of the pulmonary trunk, extending into the left and right pulmonary arteries.
If large enough, it can completely obstruct both left and right pulmonary arteries resulting in right heart failur...
Article
Page kidney
Page kidney, or Page phenomenon, refers to systemic hypertension secondary to extrinsic compression of the kidney by a subcapsular collection, e.g. hematoma, seroma, or urinoma.
Clinical presentation
Patients present with hypertension, which may be recognized acutely after an inciting event or...
Article
Fibromuscular dysplasia
Fibromuscular dysplasia (FMD) is a heterogeneous group of vascular lesions characterized by idiopathic, non-inflammatory, and non-atherosclerotic angiopathy of small and medium-sized arteries.
Epidemiology
The prevalence is unknown 7. It is most common in young women with a female to male rati...
Article
Tuberous sclerosis
Tuberous sclerosis (TS), also known as tuberous sclerosis complex (TSC) or Bourneville disease, is a phakomatosis (neurocutaneous disorder) characterized by the development of multiple benign tumors of the embryonic ectoderm (e.g. skin, eyes, and nervous system).
Epidemiology
Tuberous sclerosi...
Article
Thoracic aorta
The thoracic aorta is the most superior division of the aorta and is divided into three sections:
ascending aorta
aortic arch
descending aorta
The thoracic aorta begins at the aortic valve, located obliquely just to the left of the midline at the level of the third intercostal space. It term...
Article
Stanford classification of aortic dissection
The Stanford classification, along with the DeBakey classification, is used to separate aortic dissections into those that need surgical repair, and those that usually require only medical management 7.
Both the Stanford and DeBakey systems can be used to describe all forms of an acute aortic s...
Article
Situs inversus
Situs inversus, (rare plural: sitūs inversi) short form of the Latin “situs inversus viscerum”, is a term used to describe the inverted position of chest and abdominal organs.
Terminology
The condition is called situs inversus totalis when there is a total transposition of abdominal and thorac...
Article
Scleroderma
Scleroderma, also known as systemic sclerosis, is an autoimmune connective tissue disorder characterized by multisystem fibrosis and soft tissue calcification. As such, it affects many separate organ systems, which are discussed separately:
musculoskeletal manifestations of scleroderma
pulmona...
Article
Rheumatic fever
Rheumatic fever is an illness caused by an immunological reaction following group A streptococcal infection.
Epidemiology
Risk factors include:
children and adolescents aged 5 to 15 years
developing nations where antibiotic prescription is low 1
poverty, overcrowding
Clinical presentation...