Sézary syndrome
Citation, DOI, disclosures and article data
Citation:
Yap J, Di Muzio B, Bell D, et al. Sézary syndrome. Reference article, Radiopaedia.org (Accessed on 15 Jan 2025) https://doi.org/10.53347/rID-17894
Permalink:
rID:
17894
Article created:
Disclosures:
At the time the article was created Yuranga Weerakkody had no recorded disclosures.
View Yuranga Weerakkody's current disclosures
Last revised:
Disclosures:
At the time the article was last revised Joshua Yap had no recorded disclosures.
View Joshua Yap's current disclosures
Revisions:
6 times, by
6 contributors -
see full revision history and disclosures
Systems:
Sections:
Tags:
Synonyms:
- Sezary's syndrome
- Sezary's disease
- Sezary disease
Sézary syndrome (SS) is a type of primary cutaneous T-cell lymphoma.
Clinical presentation
It is clinically characterized by an extensive erythematous rash covering most of the body as well as the presence of malignant lymphocytes in the blood.
History and etymology
It is named after Albert Sézary, French dermatologist (1880-1956) 5.
Differential diagnosis
- other types of primary cutaneous lymphomas
- mycosis fungoides: no malignant lymphocytes in the blood
- metastases
References
- 1. Kulin PA, Marglin SI, Shuman WP et-al. Diagnostic imaging in the initial staging of mycosis fungoides and Sézary syndrome. Arch Dermatol. 1990;126 (7): 914-8. Arch Dermatol (link) - Pubmed citation
- 2. Howlett DC, Wong WL, Smith NP et-al. Computed tomography in the evaluation of cutaneous T-cell lymphoma. Eur J Radiol. 1995;20 (1): 39-42. Eur J Radiol (link) - Pubmed citation
- 3. Tsai EY, Taur A, Espinosa L et-al. Staging accuracy in mycosis fungoides and sezary syndrome using integrated positron emission tomography and computed tomography. Arch Dermatol. 2006;142 (5): 577-84. doi:10.1001/archderm.142.5.577 - Pubmed citation
- 4. Foster GH, Eichenhorn MS, Van slyck EJ. The Sézary syndrome with rapid pulmonary dissemination. Cancer. 1985;56 (5): 1197-8. - Pubmed citation
- 5. BOLGERT M. Albert Sézary, 1880-1856. (1957) A.M.A. archives of dermatology. 75 (5): 782-3. Pubmed
Incoming Links
Related articles: Lymphoma
- overview of lymphoma
- WHO classification of tumors of hematopoietic and lymphoid tissues
- location-specific lymphomas
- central nervous system
- head and neck lymphoma
- thoracic lymphoma
- gastrointestinal lymphoma
- hepatobiliary lymphoma
- genitourinary lymphoma
- musculoskeletal lymphoma
- cutaneous lymphoma
- multi-regional
- lymphoma staging
Unable to process the form. Check for errors and try again.