Chronic lung disease in sickle cell anemia is one of the pulmonary complications that can occur with sickle cell disease.
For a general discussion of sickle cell disease, please refer to sickle cell disease.
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Clinical presentation
Patients often present slow progressive decline in pulmonary function in individuals affected with HbSS. Individuals usually have a preceding history of several events of acute chest syndrome of sickle cell disease.
Pathology
Established fibrotic lung changes from repeated episodes of pulmonary infective and micro-occlusive events.
Radiographic features
HRCT
May show interstitial changes with septal thickening, wedge opacities, and traction bronchiectasis.
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