Sickle cell disease (chronic lung disease)
Updates to Article Attributes
Body
was changed:
Chronic lung disease is one of the pulmonary complicationcomplications that can occur with sickle cell disease.
Clinical presentation
Patients often present slow progressive decline in pulmonary function in individuals affected with HbSS. IndividuallyIndividuals usually have a preceding history of several events of acute chest syndrome of sickle cell disease.
Pathology
Established fibrotic lung changes from repeated episodes of pulmonary infective and micro-occlusive events.
Radiographic features
HRCT
May show interstitial changes with septal thickening, wedge opacities and traction bronchiectasis.
See also
-<p><strong>Chronic lung disease</strong> is one of the pulmonary complication that can occur with <a href="/articles/sickle-cell-disease" title="Sickle cell disease">sickle cell disease</a>.</p><h4>Clinical presentation</h4><p>Patients often present slow progressive decline in pulmonary function in individuals affected with HbSS. Individually usually have a preceding history of several events of <a href="/articles/acute-chest-syndrome-in-sickle-cell-disease" title="Acute chest syndrome in sickle cell disease">acute chest syndrome of sickle cell disease</a>. </p><h4>Pathology </h4><p>Established fibrotic lung changes from repeated episodes of pulmonary infective and micro-occlusive events.</p><h4>Radiographic features</h4><h5>HRCT</h5><p>May show interstitial changes with septal thickening, wedge opacities and <a href="/articles/traction-bronchiectasis" title="traction bronchiectasis">traction bronchiectasis</a>.</p><h4>See also</h4><ul style="padding-top: 0px; padding-right: 0px; padding-bottom: 0px; padding-left: 0px; margin-top: 0px; margin-right: 0px; margin-bottom: 14px; margin-left: 40px; "><li style="padding-top: 0px; padding-right: 0px; padding-bottom: 0px; padding-left: 0px; margin-top: 0px; margin-right: 0px; margin-bottom: 0px; margin-left: 0px; ">-<a href="/articles/sickle-cell-disease" title="Sickle cell disease" style="padding-top: 0px; padding-right: 0px; padding-bottom: 0px; padding-left: 0px; margin-top: 0px; margin-right: 0px; margin-bottom: 0px; margin-left: 0px; color: rgb(63, 117, 216); text-decoration: none; ">sickle cell disease (general article)</a><ul style="padding-top: 0px; padding-right: 0px; padding-bottom: 0px; padding-left: 0px; margin-top: 0px; margin-right: 0px; margin-bottom: 14px; margin-left: 40px; ">-<li style="padding-top: 0px; padding-right: 0px; padding-bottom: 0px; padding-left: 0px; margin-top: 0px; margin-right: 0px; margin-bottom: 0px; margin-left: 0px; "><a href="/articles/acute-chest-syndrome-in-sickle-cell-anaemia" title="Acute chest syndrome in sickle cell disease">acute chest syndrome in sickle cell disease</a></li>-<li style="padding-top: 0px; padding-right: 0px; padding-bottom: 0px; padding-left: 0px; margin-top: 0px; margin-right: 0px; margin-bottom: 0px; margin-left: 0px; ">-<a href="/articles/chronic-lung-disease-in-sickle-cell-anaemia" title="Chronic lung disease in sickle cell anaemia" style="padding-top: 0px; padding-right: 0px; padding-bottom: 0px; padding-left: 0px; margin-top: 0px; margin-right: 0px; margin-bottom: 0px; margin-left: 0px; color: rgb(63, 117, 216); text-decoration: none; "></a><a href="/articles/skeletal-manifestations-of-sickle-cell-disease" title="Skeletal manifestations of sickle cell disease" style="padding-top: 0px; padding-right: 0px; padding-bottom: 0px; padding-left: 0px; margin-top: 0px; margin-right: 0px; margin-bottom: 0px; margin-left: 0px; color: rgb(63, 117, 216); text-decoration: none; ">skeletal manifestations of sickle cell disease</a>-</li>-<li style="padding-top: 0px; padding-right: 0px; padding-bottom: 0px; padding-left: 0px; margin-top: 0px; margin-right: 0px; margin-bottom: 0px; margin-left: 0px; ">-<a href="/articles/skeletal-manifestations-of-sickle-cell-disease" title="Skeletal manifestations of sickle cell disease" style="padding-top: 0px; padding-right: 0px; padding-bottom: 0px; padding-left: 0px; margin-top: 0px; margin-right: 0px; margin-bottom: 0px; margin-left: 0px; color: rgb(63, 117, 216); text-decoration: none; "></a><a href="/articles/abdominal-manifestations-of-sickle-cell-disease" title="Abdominal manifestations of sickle cell disease" style="padding-top: 0px; padding-right: 0px; padding-bottom: 0px; padding-left: 0px; margin-top: 0px; margin-right: 0px; margin-bottom: 0px; margin-left: 0px; color: rgb(63, 117, 216); text-decoration: none; ">abdominal manifestations of sickle cell disease</a>-</li>-<li style="padding-top: 0px; padding-right: 0px; padding-bottom: 0px; padding-left: 0px; margin-top: 0px; margin-right: 0px; margin-bottom: 0px; margin-left: 0px; ">-<a href="/articles/abdominal-manifestations-of-sickle-cell-disease" title="Abdominal manifestations of sickle cell disease" style="padding-top: 0px; padding-right: 0px; padding-bottom: 0px; padding-left: 0px; margin-top: 0px; margin-right: 0px; margin-bottom: 0px; margin-left: 0px; color: rgb(63, 117, 216); text-decoration: none; "></a><a href="/articles/cerebral-manifestations-of-sickle-cell-disease" title="Cerebral manifestations of sickle cell disease" style="padding-top: 0px; padding-right: 0px; padding-bottom: 0px; padding-left: 0px; margin-top: 0px; margin-right: 0px; margin-bottom: 0px; margin-left: 0px; color: rgb(63, 117, 216); text-decoration: none; ">cerebral manifestations of sickle cell disease</a>-</li>- +<p><strong>Chronic lung disease</strong> is one of the pulmonary complications that can occur with <a href="/articles/sickle-cell-disease">sickle cell disease</a>.</p><h4>Clinical presentation</h4><p>Patients often present slow progressive decline in pulmonary function in individuals affected with HbSS. Individuals usually have a preceding history of several events of <a href="/articles/acute-chest-syndrome-in-sickle-cell-disease">acute chest syndrome of sickle cell disease</a>. </p><h4>Pathology </h4><p>Established fibrotic lung changes from repeated episodes of pulmonary infective and micro-occlusive events.</p><h4>Radiographic features</h4><h5>HRCT</h5><p>May show interstitial changes with septal thickening, wedge opacities and <a href="/articles/traction-bronchiectasis">traction bronchiectasis</a>.</p><h4>See also</h4><ul><li>
- +<a href="/articles/sickle-cell-disease">sickle cell disease (general article)</a><ul>
- +<li><a href="/articles/acute-chest-syndrome-in-sickle-cell-anaemia">acute chest syndrome in sickle cell disease</a></li>
- +<li><a href="/articles/skeletal-manifestations-of-sickle-cell-disease">skeletal manifestations of sickle cell disease</a></li>
- +<li><a href="/articles/abdominal-manifestations-of-sickle-cell-disease">abdominal manifestations of sickle cell disease</a></li>
- +<li><a href="/articles/cerebral-manifestations-of-sickle-cell-disease">cerebral manifestations of sickle cell disease</a></li>