Splenic haemangiomatosis involves multiple, diffuse splenic haemangiomas replacing its entire parenchyma. It is a very rare entity.
It can occur as a manifestation of systemic angiomatosis or, less commonly, confined to the spleen (diffuse isolated splenic haemangiomatosis). There is total or subtotal replacement of the splenic parenchyma by a vascular proliferation featuring the usual morphological findings of haemangiomas.
Reported associations include
Patients may clinically present with
Non sensitive and non specific but may show
- calcifications in left hypochondriac region
- features of splenomegaly
- solid hyperechoic masses
- complex echogenic mass with cystic areas
- non contrast - well defined iso-hypodense masses
- post contrast - lesions show homogenous enhancement
Signal characteristics of individual lesions include
Typical uncomplicated lesions
- T1: most are hypo-isointense while some are hyper intense
- T2: hyper- intense
There is variable intensity if there is associated thrombosis, infarction and/or haemorrhage
In general, diffuse splenic hemangiomatosis is a benign lesion and may have an asymptomatic course. It however can present with associated complications such as some of those mentioned above.
- haemangioma - general
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