Splenic haemangiomatosis

Splenic haemangiomatosis is a situation there are multiple, diffuse splenic haemangiomas replacing its entire parenchyma. It is a very rare entity .

It can occur as a manifestation of systemic angiomatosis or, less commonly, confined to the spleen (diffuse isolated splenic haemangiomatosis). There is total or subtotal replacement of the splenic parenchyma by a vascular proliferation featuring the usual morphological findings of haemangiomas.

Associations

Reported associations include

Patients may clinically present with 

Plain film

Non sensitive and non specific but may show

  • calcifications in left hypochondriac region
  • features of splenomegaly
Ultrasound

May show

  • solid hyperechoic masses
  • complex echogenic mass with cystic areas
  • splenomegaly
CT
  • non contrast - well defined iso-hypodense masses
  • post contrast -  lesions show homogenous enhancement
MRI

Signal characteristics of individual lesions include

Typical uncomplicated lesions

  • T1 - most are hypo-isointense while some are hyper intense
  • T2 - hyper- intense

There is variable intensity if there is associated thrombosis, infarction and/or haemorrhage

In general, diffuse splenic hemangiomatosis is a benign lesion and may have an asymptomatic course. It however can present with associated complications such as some of those mentioned above.

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Article Information

rID: 25583
Sections: Gamuts, Pathology
Tag: cases
Synonyms or Alternate Spellings:
  • Hemangiomatosis of spleen
  • Multiple splenic hemangiomas
  • Hemangiomatous transformation of the spleen
  • Multiple splenic haemangiomas

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