When present, it is seen in continuity with a long syrinx that demonstrates syringomyelia, syringobulbia and syringopontia 1. As with syringopontia, the syrinx may or may not have a communication with the fourth ventricle 1. In rare cases when it is present without syringomyelia, the term 'keyhole aqueduct syndrome' has been employed by some authors 2.
There are numerous causes and associations, and these are discussed in more depth in the general article on syrinx.
Syringomesencephaly has the same radiographic characteristics on all imaging modalities as any other syrinx 1. See syrinx for an in-depth discussion of these characteristics.
Treatment and prognosis
When symptomatic, neurosurgical intervention may be required 1.
- 1. Menezes AH, Greenlee JD, Longmuir RA, Hansen DR, Abode-Iyamah K. Syringohydromyelia in association with syringobulbia and syringocephaly: case report. Journal of neurosurgery. Pediatrics. 15 (6): 657-61. doi:10.3171/2014.11.PEDS14189 - Pubmed
- 2. de la Monte SM, Horowitz SA, Larocque AA, Richardson EP. Keyhole Aqueduct Syndrome. Archives of Neurology. 43 (9): 926. doi:10.1001/archneur.1986.00520090056017