Syringopontia is a rare entity and refers to a syrinx that extends into the pons 1. In rare cases when syringopontia is present without syringomyelia, the term keyhole aqueduct syndrome has been employed by some authors 2,3.
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Clinical presentation
Patients with this condition demonstrate a wide variety of neurological symptoms localised to the pons, medulla oblongata, and spinal cord, depending on where exactly the syrinx is located 1. For example, in keyhole aqueduct syndrome, the most common clinical features include internuclear ophthalmoplegia and nystagmus 3.
Pathology
When present, it is seen in continuity with a long syrinx that demonstrates syringomyelia and syringobulbia 1. The syrinx may or may not have a communication with the fourth ventricle 1.
There are numerous causes and associations, and these are discussed in more depth in the general article on syrinx.
Radiographic features
Syringopontia has the same radiographic characteristics on all imaging modalities as any other syrinx 1. See syrinx for an in-depth discussion of these characteristics.
Treatment and prognosis
When symptomatic, neurosurgical intervention may be required 1.
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