Tilted telephone receiver sign

Last revised by Mohammad Taghi Niknejad on 14 Sep 2024

The tilted telephone receiver sign (TTRS) has been described as a specific imaging feature of PHACES syndrome in fetal MRI 1

On the coronal plane, the TTRS sign is described as:

  • upward displaced unilateral hypoplastic cerebellar hemisphere;

  • asymmetric dilated 4th ventricle connected to as ipsilateral retrocerebellar cyst

  • elongated oblique connection between the hemispheres formed upwardly rotated and deviated vermis merging with the contralateral cerebellar peduncle

It shouldn't be confused with the telephone receiver deformity which is a characteristic bowing of the shaft of the long bones, usually the humeri or femora, seen in thanatophoric dysplasia.

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