Tumor necrosis factor receptor-associated periodic syndrome

Last revised by David Luong on 12 Jul 2021

Citation, DOI, disclosures and article data

Citation:

Weerakkody Y, Luong D, Elfeky M, Tumor necrosis factor receptor-associated periodic syndrome. Reference article, Radiopaedia.org (Accessed on 23 Apr 2024) https://doi.org/10.53347/rID-71049

DOI:

https://doi.org/10.53347/rID-71049

Permalink:

https://radiopaedia.org/articles/71049?iframe=true

rID:

71049

Article created:

16 Sep 2019, Yuranga Weerakkody ◉

Disclosures:

At the time the article was created Yuranga Weerakkody had no recorded disclosures.

View Yuranga Weerakkody's current disclosures

Last revised:

12 Jul 2021, David Luong ◉

Disclosures:

At the time the article was last revised David Luong had no recorded disclosures.

View David Luong's current disclosures

Revisions:

3 times, by 3 contributors - see full revision history and disclosures

Systems:

Vascular

Sections:

Syndromes

Tags:

cases

Synonyms:

TRAPS
TNF receptor associated periodic syndrome
Tumour necrosis factor receptor-associated periodic fever syndrome

Tumor necrosis factor receptor-associated periodic syndrome (or sometimes abbreviated as TRAPS) is a condition characterized by recurrent (periodic) episodes of fever as well as a spectrum of dermatologic findings that includes migratory patches, edematous plaques, periorbital edema, and/or conjunctivitis.

Pathology

It is characterized by a perivascular dermal infiltrate of lymphocytes and monocytes. Its thought to be dominantly inherited mutations in TNFRSF1A, the gene encoding the 55-kDa tumor necrosis factor (TNF) receptor.

Tumor necrosis factor receptor-associated periodic syndrome

Citation, DOI, disclosures and article data

Pathology

See also

References

Incoming Links

Promoted articles (advertising)