Uhl anomaly is an unusual cardiac disorder which affects the right ventricle where there is almost complete absence of right ventricular myocardium, normal tricuspid valve, and preserved septal and left ventricular myocardium.
History and etymology
It is named after Henry S D Uhl, who first described the condition in 1952 3.
Imaging differential considerations include:
- 1. Mazur W, Siegel MJ, Miszalski-Jamka T et-al. CT Atlas of Adult Congenital Heart Disease. Springer. ISBN:1447150872. Read it at Google Books - Find it at Amazon
- 2. Gerlis LM, Schmidt-Ott SC, Ho SY et-al. Dysplastic conditions of the right ventricular myocardium: Uhl's anomaly vs arrhythmogenic right ventricular dysplasia. Br Heart J. 1993;69 (2): 142-50. Free text at pubmed - Pubmed citation
- 3. Uhl HS. A previously undescribed congenital malformation of the heart: almost total absence of the myocardium of the right ventricle. Bull Johns Hopkins Hosp. 2003;91 (3): 197-209. Pubmed citation
- 4. Greer ML, MacDonald C, Adatia I. MRI of Uhl's anomaly. Circulation. 2000;101 (24): E230-2. Circulation (full text) - doi:10.1161/01.CIR.101.24.e230 - Pubmed citation