Unilateral pulmonary vein atresia

Unilateral pulmonary vein atresia is a type of pulmonary vein atresia.

It results from failure of incorporation of the common pulmonary vein into the left atrium. There is no recognised right or left predilection.

The condition usually present in infancy or childhood with recurrent episodes of pneumonia and/or haemoptysis. Presentation in adulthood does occur but is uncommon.

Chest radiographic findings are not specific but may be seen as a small ipsilateral hemithorax and unilateral reticular opacities with septal lines.

Allows direct visualisation of absence of affected pulmonary vein. CT may additionally show:

  • small ipsilateral hemithorax
  • ipsilateral mediastinal shift
  • small ipsilateral pulmonary artery

Other parenchymal findings (although each on its own is non-specific) include 1:

Shows decreased perfusion to affected lung.

Pneumonectomy is sometimes indicated once symptoms or complications are present.

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Article information

rID: 31973
Section: Pathology
Synonyms or Alternate Spellings:
  • Unilateral atresia of pulmonary vein
  • Unilateral atresia of the pulmonary vein

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