Caroli disease with medullary sponge kidney and nephrocalcinosis
Presentation
Obstructive jaundice
Patient Data
Note: This case has been tagged as "legacy" as it no longer meets image preparation and/or other case publication guidelines.
MRI reveals intrahepatic and extrahepatic cystic dilatations of biliary tract with multiple large calculi.
Incidental detection of medullary sponge kidney.
Case Discussion
MRI reveals intrahepatic and extrahepatic cystic dilatations of the biliary tract with multiple large calculi. Incidental detection of medullary sponge kidney. Renal USG performed subsequently also revealed nephrocalcinosis.
Isolated case reports of association of Caroli disease with renal cystic disease are scattered in the English literature. There is also an association of oro-facial-digital syndrome with cystic disease of the kidneys and the biliary tree.