Dyke-Davidoff-Masson syndrome

Discussion:

The MRI features most consistent with Dyke-Davidoff-Masson syndrome with right cerebral hemiatrophy, cystic encephalomalacia with surrounding gliosis and compensatory thickening of the calvarium.

Dyke-Davidoff-Masson syndrome refers to hemicerebral atrophy/hypoplasia secondary to brain insult usually in the fetal or early childhood period and characterized by ipsilateral compensatory hypertrophy of the skull vault and contralateral hemiparesis.

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