What tends to be most frequent cause of death of patients with Marfan syndrome?
Cardiovascular complications tend to be most frequent cause of death of patients with Marfan syndrome.1
What ist the modality of choice to monitor vascular disoreders in young patients with connective tissue disorders?
MRI has the advantage of not requiring ionising radiation or large volumes of iodinated contrast. This is particularly advantageous in young patients with connective tissue disorders.
Aneurysm of the descending thoracic aorta with a diamter of 45 mm over a length of 50 mm. Note that both subclavian arteries (left > right) are also dilated.