What are the features of Zinner syndrome?
(1 )unilateral renal agenesis; (2) ipsilateral ejaculatory duct obstruction; (3) ipsilateral seminal vesicle cyst
What is the pathophysiology?
Maldevelopment of the distal part of the mesonephric duct results in atresia of the ejaculatory duct (leading to obstruction and dilatation of the seminal vesicle) while abnormal ureteral budding (leads to renal agenesis/dysplasia)
- right sided renal agenesis
- cystic dilatation of the seminal vesicle on the right side
- dilatation of the right sided vas deferens from posterior aspect of prostate extending into the right inguinal canal;
- dilated duct is seen to indent the posterior wall of urinary bladder
- right sided ectopic ureter opening into the right vas deferens inferiorly; superiorly it has a blind end
- left kidney is normal
- point to note is the high signal intensity within the dilated ducts on T1W images probably due to high proteinaceous content as a result of stasis