Usual interstitial pneumonia
Idiopathic pulmonary fibrosis is more common in smokers. The disease has a poor prognosis with median survival of 2 to 3 years.
Diagnostic criteria include:
Major criteria
- exclusion of known cause of pulmonary fibrosis
- restrictive pattern in pulmonary function test
- bibasilar reticulation with minimal ground glass opacity
- negative bronchial lavage report for another disease
Minor criteria
- age >50 years
- dyspnea on exertion with insidious onset
- duration of illness>3 months
- Velcro Like respiratory crackles
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