Usual interstitial pneumonia

Discussion:

Idiopathic pulmonary fibrosis is more common in smokers. The disease has a poor prognosis with median survival of 2 to 3 years. 

Diagnostic criteria include:

Major criteria

  • exclusion of known cause of pulmonary fibrosis
  • restrictive pattern in pulmonary function test
  • bibasilar reticulation with minimal ground glass opacity
  • negative bronchial lavage report for another disease

Minor criteria

  • age >50 years
  • dyspnea on exertion with insidious onset
  • duration of illness>3 months
  • Velcro Like respiratory crackles
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