Posterior fossa hemangioblastoma

Case contributed by Subash Thapa
Diagnosis almost certain

Presentation

Progressive headache and ataxia.

Patient Data

Age: 35 years
Gender: Female

MRI Brain

mri

Well defined cystic mass measuring 4.43 x 3.71 cm involving the left cerebellum and showing mild perilesional edema and mass effect with compression of the fourth ventricle causing hydrocephalus.

There is an eccentric strongly enhancing nodule lesion abutting the lateral wall of the cyst.

There are prominent vessels overlying the nodule.

No calcification or hemorrhage

Case Discussion

MRI shows typical features of posterior fossa hemangioblastoma. Waiting for histological confirmation. 

Hemangioblastomas are vascular origin tumors in patients with von-Hippel Lindau (vHL) disease. 

87-97% are intracranial, 55% in the posterior fossa, and 85% in the cerebellar hemisphere

Hemangioblastomas are rare under 15 years, with a peak age between 30-65 years; similar lesions in the posterior fossa among children are pilocytic astrocytomas

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