IMPORTANT: We currently have a number of bugs related to image cropping and are actively trying to resolve them. In the meantime, we have disabled cropping. Apologies for any inconvenience. Stay informed: radiopaedia.org/chat

Dyke-Davidoff-Mason syndrome

Case contributed by Bruno Di Muzio
Diagnosis certain

Presentation

Long history of well-controlled epilepsy. Two recent seizures.

Patient Data

Age: 70 years
Gender: Female

MRI Brain (selected images)

mri

These select sequences demonstrate an atrophic right hemisphere, with prominently ex vacuo dilated right lateral ventricle and gliosis/periventricular FLAIR hyperintensity. In addition, there is compensatory bony changes, with a large right frontal sinus, as well as right sided calvarial thickening and elevated petrous ridge. The falx is also deviated to the right.

The remainder study (not shown) is unremarkable. 

Case Discussion

This brain MRI demonstrates findings in keeping with Dyke-Davidoff-Mason syndrome: atrophy or hypoplasia of one cerebral hemisphere (hemiatrophy). In radiology, this so-called syndrome is more likely to represent a group of radiological findings that expresses a possible sequela of a fetal or early childhood period brain insult

How to use cases

You can use Radiopaedia cases in a variety of ways to help you learn and teach.

Creating your own cases is easy.

Updating… Please wait.

 Unable to process the form. Check for errors and try again.

 Thank you for updating your details.