Hypertrophic cardiomyopathy with cor triatriatum


This is a case of asymmetric hypertrophic cardiomyopathy with associated systolic anterior motion (SAM) of the anterior mitral leaflet, which contributes to left ventricular outflow tract (LVOT) obstruction. 

Hypertrophic cardiomyopathy is a heterogeneous group of diseases related to sarcomere gene mutations. It affects one of every 500 adults and is the most common cause of sudden death in young athletes. Asymmetric hypertrophic cardiomyopathy is the most common morphologic variant of this disease.

Cor triatriatum is also demonstrated in this case. It is a rare congenital anomaly known to be associated with other inherited cardiac diseases. To the best of our knowledge, only few cases of cor triatriatum coexisting with hypertrophic cardiomyopathy have been reported.