Presentation
Seizures
Patient Data
Age: 3 weeks
Gender: Female
From the case:
Hemimegalencephaly
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The left hemisphere totally enlarged.
The cortex of the enlarged brain is malformed: there is no gray/white matter differentiation, sulci and gyri looks smooth and shallow.
The white matter is also abnormal: T2-hypointense and T1-hyperintense subcortical signals.
Compensatory enlargement of the left ventricle.
Case Discussion
There are typical features of hemimegalencephaly causing intractable seizures since birth.