What is the distribution of cysts in Birt-Hogg-Dubé syndrome?
What is the pattern of heritability of Birt-Hogg-Dubé syndrome?
For what renal cancers are patients with Birt-Hogg-Dubé syndrome at greater risk?
Chromophobe renal cell carcinoma and renal oncocytoma.
Chest CT shows multiple large, thin-walled cysts in a lower lobe predominant distribution. Pleural thickening and staple lines along the lower lobes, middle lobe, and lingula are expected sequelae of pleurodesis and bullectomies. The absence of a pneumothorax is the most important pertinent negative in this case. There is also a small tracheal diverticulum, which is stable when compared to remote prior studies.