What are the two 'types' of this condition, and from whose perspective are they named?
Fenestral and retrofenestral (from the perspective of otolaryngologist looking into the middle ear).
How does this condition usually present?
Hearing loss, typically conductive for fenestral type.
True or false: the appearance of this case is typical of the active phase of disease.
True. Eventually the region may become sclerotic with fusion of the foot plate of the stapes.
CT through the left temporal bone demonstrates a circumscribed region of demineralisation immediately anterior to the oval window, in the bone between the cochlea and vestibule.