Liver laceration from gunshot in a thalassemia intermedia patient

Discussion:

Young male shot through the abdomen with an AAST grade IV liver laceration showing active arterial bleeding.

Incidentally, the patient has a diagnosis of thalassemia intermedia, a less severe form of beta thalassemia major, where there is a relatively small amount of the β chain and hemoglobin A. Accompanying intellectual disability and pervasive developmental disorder, mild pulmonary hypertension.
Underwent splenectomy of an enlarged spleen at age 13 due to recalcitrant anemia, but to no avail (baseline hemoglobin level 8 g/dL). This, together with mildly H-shaped vertebrae seen on the sagittal view, could suggest coexisting sickle cell trait: hemoglobin sickle-beta thalassemia (Hb S/β-thalassemia)

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