The most common renal mass in children is Wilms tumor, but in this case; it does not meet the radiological classic features of Wilms tumor, despite the patient age.

The presence of lymph node enlargement may raise the possibility of lymphoma.

The imaging diagnosis of renal cell carcinoma and subtypes are a challenge in a pediatric age. So accurate histologic and imaging characterization of renal cell carcinoma is important for prognosis and management.