Os odontoideum

Case contributed by Dustin Roberts
Diagnosis almost certain

Presentation

Chronic neck pain, no history of trauma.

Patient Data

Age: 55 years
Gender: Female
x-ray

Anterior translation of C2 on C1 due to non-visualized origin of the odontoid process. 
The C1 arch is intact.
Near reversal of cervical spine lordosis.
Moderately severe degenerative changes with narrowing of multiple intervertebral discs.
Multilevel neuroforaminal encroachment by posterior osteophytes.
Minimal posterior spondylolisthesis of C4-C5 and C5-6. 
No osteolytic lesion or bony erosion.

Annotated image

Annotated frontal and lateral views demonstrating the presence of an ossicle (green arrows) that lacks continuity with C2, consistent with os odontoideum.

Case Discussion

Anatomical anomalies involving the craniovertebral junction are clinically important as they give rise to potentially serious neurological deficits due to atlantoaxial instability and dislocation. Potential adverse outcomes include persistent neck pain, headaches, and transient or permanent paresis.

Anomalies involving the odontoid process are exceptionally rare, and are due to one of three etiologies: trauma, osteolysis, or congenital malformation. Congenital anomalies of the odontoid are classified into four types depending on the extent of involvement: os odontoideum, ossiculum terminale, aplasia-hypoplasia, and duplication of the dens. Of these, aplasia is the least common and only a few cases have been reported in the literature.

Our patient with no history of trauma and radiographic evidence of a small ossicle without an odontoid process likely has os odontoideum. Dynamic flexion and extension imaging studies were recommended for further risk assessment and management.

 

This case was submitted with supervision and input from:

Thomas Zung, M.D.
Staff Radiologist
Department of Radiological Sciences
Olive View - UCLA Medical Center

Soni C. Chawla, M.D.
Associate Professor
Department of Radiological Sciences
David Geffen School of Medicine at UCLA
Olive View - UCLA Medical Center

How to use cases

You can use Radiopaedia cases in a variety of ways to help you learn and teach.

Creating your own cases is easy.

Updating… Please wait.

 Unable to process the form. Check for errors and try again.

 Thank you for updating your details.