Congenital hiatus hernia is a very rare disease and congenital posterior perineal hernia is even rarer and considered one of the least common types of hernias.

The presence of both congenital hernias in the same patient suggests marked tissue laxity as in this case of cutis laxa (CL) which is a general term for a group of rare disorders named after the characteristic skin phenotype; they are multi-systemic disorders and commonly involve the visceral organs.

Repeated herniation and repositioning of the stomach that was noted in the serial follow up x-ray can cause serious respiratory distress and alarms for rapid surgical correction to avoid serious complications.