DORV double outlet right ventricle occurs when both great arteries arise entirely or predominantly from the RV.

Several types of DORV exist according to the location of the VSD, the spatial relationship of the great arteries and whether or not there is an outflow obstruction.

Pulmonary stenosis is the most common associated cardiac anomaly.

Chromosomal anomalies are found in some fetuses (12% up to 40%) such as trisomies 18,13 and 22q1.1 microdeletion (region in the long arm (q) of chromosome 22).

Tetralogy of Fallot and transposition of the great arteries are two main differential diagnoses for DORV. 

Subpulmonic VSD and aortic coarctation are associated with suboptimal postsurgical outcomes in DORV.