Contrast-enhanced MRI reveals expansile intramedullary lesion between T3 and T6, isointense on T1-WI, hyperintense on T2-WI, with diffuse heterogeneous enhancement. The mass is slightly eccentric to the right side on the axial image, and determines expansion of the thoracic spinal cord, at T3-T6. There is an extensive septated syringohydromyelia, resulting in a thin rim of cervical and thoracic cord, as well as conus medullaris.