The patient had a negative family history of Von-Hipple disease. Genetic testing showed an absent mutation in the VHL tumor suppressor gene.

Hemangioblastomas are benign vascular tumors commonly found in the posterior fossa or the spinal cord, whereas supratentorial hemangioblastomas with meningeal involvement are extremely rare. Hemangioblastomas are common in Von-Hipple disease, but they might occur sporadically.

Supratentorial hemangioblastomas are usually solid and are mostly located in the frontal lobe ^1.

Characteristic imaging findings include a bright signal on T2 WI, prominent flow voids, and vivid post-contrast enhancement. Also, peritumoral edema is usually observed.

Differential diagnosis includes angiomatous meningioma, hemangiopericytoma, and hypervascular metastatic lesions such as renal cell carcinoma metastasis.

Preoperative diagnosis can be helpful to decrease blood loss at surgery via preoperative embolization ².