Aberrant left pulmonary artery (pulmonary sling)

Case contributed by Dr Vincent Tatco

Presentation

Patient with wheezing and feeding problems referred to evaluate for airway stenosis.

Patient Data

Age: 3 months
Gender: Female

The heart is normal in size and positioned in the right side of the mediastinum. The cardiac apex is directed to the right with the left ventricle located anteriorly and still to the left of the right ventricle. There is atrio-ventricular and ventriculo-arterial concordance. These findings are reflective of cardiac dextroversion. The atria and ventricles are normal in size without dilatation or hypertrophy of the musculature.

A single right-sided aortic root is detected with its arch coursing from right to left anterior to trachea. The descending aorta is left-sided. There is minimal denting of the anterior aspect of the mid trachea as the arch crosses the trachea.

The pulmonary trunk, measuring 1.4 cm in widest transverse diameter, is larger than the aortic root , which measures 1 cm. The right pulmonary artery branch measures 0.5 cm. The left pulmonary artery branch emanates from the right pulmonary artery and courses behind the trachea at the level of the carina and anterior to the esophagus. This area of crossing along the distal trachea causes mild narrowing of the lumen.  These findings are consistent with pulmonary sling. 

The inferior vena cava, right and persistent left superior vena cavae drain into the right atrium.

The trachea is midline in location. The tracheal stenosis at the mid segment is approximately 30% due to the above-mentioned crossing of the aortic arch. The pulmonary sling described above causes approximately 16% distal tracheal stenosis. There is also narrowing at the branch point of the right main stem bronchus.

Both lungs show mosaic pattern of attenuation suggestive of air trapping. 

Annotated image

Axial MIP image demonstrates the aberrant left pulmonary artery (pulmonary sling) arising from the right pulmonary artery passing between the trachea and esophagus. 

Case Discussion

Aberrant left pulmonary artery, also known as pulmonary sling, is characterized by anomalous origin of the left pulmonary artery from the right pulmonary artery. To reach the left lung, the anomalous left pulmonary artery courses over the proximal portion of the right mainstem bronchus, behind the trachea, and in front of the esophagus to the left pulmonary hilum. In this process, it forms a sling that compresses the trachea and right main stem bronchus, producing upper airway symptoms.

 

PlayAdd to Share

Case information

rID: 42323
Case created: 15th Jan 2016
Last edited: 16th Aug 2017
Inclusion in quiz mode: Included

Updating… Please wait.
Loadinganimation

Alert accept

Error Unable to process the form. Check for errors and try again.

Alert accept Thank you for updating your details.