Presentation
Known patient with Alagille syndrome, branch pulmonary artery stenosis and a left pulmonary artery (LPA) stent.
Patient Data
Age: 6 years
Gender: Male
From the case:
Alagille syndrome
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Stable appearance of the median sternotomy wires with the most inferior wire fractured. Stable pulmonary artery vascular stent.
No focal areas of consolidation or pleural effusions are identified.
The cardiac silhouette is not enlarged
Case Discussion
Surgery initially, thereafter multiple cardiac interventions for pulmonary artery stenosis with stents.