Alagille syndrome

Case contributed by Jayanth Keshavamurthy
Diagnosis certain


Known patient with Alagille syndrome, branch pulmonary artery stenosis and a left pulmonary artery (LPA) stent.

Patient Data

Age: 6 years
Gender: Male

Stable appearance of the median sternotomy wires with the most inferior wire fractured. Stable pulmonary artery vascular stent. 

No focal areas of consolidation or pleural effusions are identified.

The cardiac silhouette is not enlarged

Case Discussion

Surgery initially, thereafter multiple cardiac interventions for pulmonary artery stenosis with stents.

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