ALCAPA in adult

Case contributed by Dr Vinay V Belaval

Presentation

Exertional chest pain.

Patient Data

Age: 40 years
Gender: Male
CT

SEGMENTAL ANALYSIS OF CORONARY ARTERIES:

Right dominant coronary circulation.

ANOMALOUS ORIGINS / COURSE: There is an anomalous origin of the left main coronary artery (LMCA) from the posterior wall of the proximal main pulmonary artery (8.4 mm above the pulmonary valve level) – compatible with ALCAPA (anomalous left coronary artery from pulmonary artery).

LMCA trifurcates into left anterior descending (LAD), left circumflex (LCX) and ramus intermedius (RI) arteries.

Multiple arterial collaterals are noted between the left and right coronary artery systems, mainly between the diagonal & septal branches of LAD and acute marginal branch of RCA. Multiple arterial collaterals are also noted between RCA and LAD & LCX in the interventricular septum and in myocardium.

LEFT MAIN: LMCA measures 11.8 mm in diameter at the level of ostium and 2.7 cm in length. It trifurcates into LAD, LCx and ramus intermedius (RI).

LEFT ANTERIOR DESCENDING:

Type: III

Proximal: dilated measuring 11.2 mm in diameter. No stenosis.

Mid and Distal: Normal

Diagonals: D1 is a good caliber, early branch measuring 7 mm in diameter. It is normal.

 

LEFT CIRCUMFLEX:

Proximal: Dilated measuring 7.3 mm in diameter. Courses posteriorly from origin to enter into the left AV groove.

Distal: Normal

Obtuse marginals: OM1 is normal.

 

RIGHT CORONARY:

Proximal: Fusiform aneurismal dilatation noted measuring 19 mm in diameter. It courses anteriorly and to the left to reach anterior to main pulmonary artery and then courses back to enter into right atrio-ventricular groove. No thrombus.

Mid: Dilated measuring 13.2 mm in diameter.

Distal: Fusiform aneurismal dilatation noted measuring 20 mm in diameter

Posterior descending: Two in number, ectatic and are normal.  

Posterolateral ventricular branch: Normal

 

Case Discussion

Anomalous origin of left coronary artery from pulmonary artery (ALCAPA) in an adult is accompanied by multiple collaterals with dilated, tortuous native coronary arteries. 

DIfferentials for dilated coronary arteries include coronary arterio-venous fistula, Kawasaki disease, and coronary cameral fistulas.

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Case information

rID: 72683
Published: 7th Dec 2019
Last edited: 7th Dec 2019
System: Cardiac
Inclusion in quiz mode: Included
Institution: Belcity Scan and Diagnostic Centre

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