Anomalous systemic arterial supply to normal lung

Presentation

Second episode of hemoptysis, with normal platelet count.

Patient Data

Age: 20 years
Gender: Female

Pulmonary pseudosequestration

CT

Area of ​​lung parenchyma connected to the tracheobronchial tree in the basal region of the left lower lobe with vascularization through an anomalous/systemic arterial branch that emerges from the descending aorta. Venous drainage is performed through the left inferior pulmonary vein.

Case Discussion

By definition, the diagnosis of true pulmonary sequestration must respect two criteria: (i) anomalous systemic vascularization and (ii) disconnection of the tracheobronchial tree, characterizing an area of ​​segregated lung tissue that is not viable for gas exchange.

In the present case, as the patient has hemoptysis and usual tracheobronchial architecture, the definitive diagnosis is a systemic artery supplying normal lung, also a congenital vascular anomaly, caused by failure of regression of the dorsal branches of the aorta that usually supply the bronchopulmonary bud during organogenesis.

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